Primary cardiac myxofibrosarcoma of the left atrial and pericardium: a case report

Abstract

Background: Primary cardiac myxofibrosarcoma is quite rare and commonly arises in the left atrial. Myxofibrosarcoma is an aggressive and has high mortality because of high rate of recurrence. It is considered that complete surgical resection is important but effective treatment options are not established. Case presentation: We report a case of 75-year-old woman who developed myxofibrosarcoma spreading to left atrial and pericardium. To prevent sudden death by obstruction of mitral valve, we performed surgical resection of the tumor. The patient developed brain metastasis at two months after surgery, and eventually passed away due to brain hemorrhage at three postoperative months. Conclusion: In this report, we described a very rare case of primary cardiac myxofibrosarcoma located not only in the left atrial but also in the pericardium. To prevent the recurrence of myxofibrosarcoma, combination of surgery, radiotherapy and chemotherapy should be needed.