Background: Granular corneal dystrophy is the commonest of the dystrophies and usually results in visual disability in the fourth or fifth decades.
Case history: A patient with granular corneal dystrophy is reported and the clinical characteristics described.
Discussion: The classical clinical features and the pathology and management of granular dystrophy are reviewed. Two unusual variations of the corneal dystrophy, namely, juvenile granular dystrophy and Avellino dystrophy, which is a concurrence of the features of granular and lattice dystrophies, are also described.