Posterior fossa tumors are frequently diagnosed in children compared to their adult counterparts, representing 54 to 70% of the cases. Tumors located in the cerebellopontine angle are rare and represent 10% of the posterior fossa lesions in children. In addition, glioblastoma multiforme is a malignant primary tumor of the central nervous system and represents 3% of the tumors in children. We present the fourth reported case of a glioblastoma multiforme, confirmed by histopathology and located in the cerebellopontine angle in a 6-year old child, which was treated with surgery and subsequently with radiotherapy and chemotherapy. Thus, the presence of a glioblastoma multiforme in the cerebellopontine angle is extremely rare and needs a high-index of suspicion in children.