Primary Ewing’s Sarcoma of the Maxilla and Zygoma: Report of a Case

Ewing’s Family of Tumors of the Sinonasal Tract and Maxillary Bone

“…None of the current cases showed nuclear pleomorphism worthy of this designation, however. Images from previous cases reported in the literature also show this nesting pattern in sinonasal EFT [13]. One possible explanation for this finding could be the rich fibrovascular nature of the native sinonasal tissue, particularly in the turbinates.…”

“…A total of 49 cases of proposed sinonasal EFT have been reported in the English language literature thus far [3,8,13,15,, 11 of which were confirmed with molecular studies [15,17,19,26,[37][38][39] and 21 of which have reported follow-up or outcomes [8, 13, 15, 19, 20, 22-26, 33, 35-37, 39, 40]. The pertinent information on previous cases of EFT with follow-up available is presented in Table 3.…”

One Approach to Facial Swelling: Tooth or Fiction

“…6 On imaging, the skull lesions classically are punched-out, with a lytic appearance and mandibular involvement simulating the appearance of "fl oating" teeth. 7 The patient's CT scan showed lytic lesions involving the mandible, with abnormal lucency at the maxillary tooth roots commonly found in LCH. With elevated liver transaminase levels, LCH became higher in the differential because liver involvement is a known sequela, especially sclerosing cholangitis, which occurred in as many as 54% of patients with multisystem LCH in 1 case series.…”

“…However, ∼2% of cases have involved the face, mostly in the mandible. 7 Of those primary tumors in the face, only 30 cases of primary maxilla involvement have been reported. 9 The most common radiologic signs in cases of primary Ewing's sarcoma involving the maxilla have been lytic changes with bone destruction and periosteal thickening, described as the "sun-ray" image.…”

Metastatic Ewing’s Sarcoma in Mandible: A Rarity

“…Ewing's sarcoma (ES) is a rare malignant small round cell tumour that primarily affects the skeletal system 1 . It accounts for 4 to10% of all types of bone cancer, with long bones and pelvis being the most common locations 1,2 . 90% occur in the first three decades of life and males are more often affected than females (male: female = 3:2).…”