Primary mucinous cystadenocarcinoma of renal pelvis: a case report

Abstract

BackgroundWe report a case of primary mucinous cystadenocarcinoma of renal pelvis which radiologically resembled large multicystic mass in 45 years old man.Case PresentationThe patient referred to our center with loin pain and progressive abdominal distention from 4 years ago. In the previous published literature, four cases of mucinous cystadenocarcinoma of renal origin have been published. Abdominal CT showed complete replacement of left kidney by a large multiloculated cystic mass accompanied with multiple large nephrolithiasis. Nephrectomy was performed and histopathology revealed covering of epithelium of renal pelvis by columnar epithelium and scattered goblet cells and mucous gland.ConclusionMucinous cystic neoplasms of kidney are rare entity and our case and few similar reported cases showed that this tumor is an unique clinicopathologic renal mass that may be classified by World Health Organization classification in the future

Incidental mucinous adenocarcinoma in situ of renal pelvis presenting as severe hydronephrosis

“…Most of the patients with this tumor are elderly males, and to the best of our knowledge, the youngest patient has been 40 years old (2). Mucinous adenocarcinoma in renal pelvis is usually presented with nonspecific symptoms such as abdominal pain (5). However a few patients have also presented with flank pain or hematuria or other symptoms related to urinary tract such as pyuria (1).…”

“…The most common neoplasm in the renal pelvis is transitional in origin, although infrequently, squamous and glandular neoplasms may arise within the renal pelvis secondary to metaplastic transformation of the transitional epithelium due to chronic obstruction and infection or irritation by stones (5). Mucinous types of adenocarcinoma in renal pelvis are the least common type of this category (1).…”

A rare renal pelvis tumor: Mucinous cystadenocarcinoma

“…Renal pelvis neoplazileri genellikle ürotelyal köken-lidir [1][2][3][4][5]. Ancak ürotelyal epitelin metaplastik deği-şikliği sonucu bu lokalizasyonda nadirde olsa skuamöz ve glandüler lezyonlar da görülebilir [1][2][3].…”

“…Ancak ürotelyal epitelin metaplastik deği-şikliği sonucu bu lokalizasyonda nadirde olsa skuamöz ve glandüler lezyonlar da görülebilir [1][2][3]. Mü-sinöz kistadenokarsinom (MKA) renal pelviste çok nadir olarak görülmekte olup literatürde bildirilen az sayıda olgu mevcuttur [1][2][3][4][5][6][7][8]. Bundan dolayı renal kistik neoplaziler hakkında bildiklerimiz oldukça sınırlıdır ve Dünya Sağlık Örgütü (DSÖ) sınıflama-sında pelvikaliksiyel sistem maligniteleri içerisinde tanımlanmamaktadır [1,2,4].…”

“…Mü-sinöz kistadenokarsinom (MKA) renal pelviste çok nadir olarak görülmekte olup literatürde bildirilen az sayıda olgu mevcuttur [1][2][3][4][5][6][7][8]. Bundan dolayı renal kistik neoplaziler hakkında bildiklerimiz oldukça sınırlıdır ve Dünya Sağlık Örgütü (DSÖ) sınıflama-sında pelvikaliksiyel sistem maligniteleri içerisinde tanımlanmamaktadır [1,2,4]. Bu yazıda 68 yaşın-daki erkek hastanın yaygın müsinöz metaplazisi gösteren pelvikaliksiyel sisteminden gelişmiş MKA klinik, radyolojik ve histopatolojik özellikleriyle beraber sunulmuştur.…”