Primary Retroperitoneal Müllerian Adenocarcinoma: A Case Report and Literature Review

Spinelli, Claudio; Strambi, Silvia; Tartaglia, Dario; Franco, Gregorio Di; Pucci,; Faviana, Pinuccia; Lencioni, Monica

doi:10.1159/000357424

Cited by 6 publications

(1 citation statement)

References 11 publications

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“…A variety of different histological subtypes of PRMA, including serous ( 7 ), endometrioid ( 1 ), clear cell ( 8 ), mucinous ( 4 ), papillary ( 2 ), mixed (serous, mucinous, and endometrioid), and even malignant mixed müllerian tumor ( 2 , 9 ), has been reported in the literature. The serous, endometrioid, and clear cell histologies were the common types ( 3 ).…”

Section: Discussionmentioning

confidence: 99%

Primary retroperitoneal müllerian adenocarcinoma: a case report

Feng,

Zhang,

Gao

2024

Front. Oncol.

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A 45-year-old woman presented with right hip pain for a month. Imaging results revealed that the left peritoneal mass was accompanied by metastases of the right sciatic branch, lung, and retroperitoneal lymph nodes. A biopsy of the left peritoneal mass was performed. The pathological morphology demonstrated clear cell adenocarcinoma. Immunohistochemical staining revealed a positive expression of keratin7 and PAX8 and a negative expression of keratin20, GCDFP-15, ER, PR, WT1, CDX2, villin, TTF-1, napsin-A, vimentin, calretinin, and GATA3. Finally, the diagnosis of primary retroperitoneal müllerian adenocarcinoma (PRMA) was confirmed. PRMA is a very rare type of primary retroperitoneal tumor. PRMA should be considered for the retroperitoneal mass.

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