Primary Synovial Osteochondromatosis of Knee (Reichel-Jones- Henderson Syndrome): A Radiological Case Report

Hussain, Zohaib; Dutta, Parul

doi:10.21276/ijcmsr.2020.5.2.24

Cited by 1 publication

(6 citation statements)

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“…The knee joint affection in PSC presents predominantly with intra-articular affection, though extra-articular or combined affection may also be present rarely [2]. PSC has been recognized as 'snowstorm knee', 'Reichel syndrome', and literature presents with only a few case reports [7,9]. Males are predominantly affected more as compared to females and commonly there is affection in the age group of 20 to 50 years with affection in children being rarely reported [2][3][4][5][6][7]10].…”

Section: Discussionmentioning

confidence: 99%

“…PSC has been recognized as 'snowstorm knee', 'Reichel syndrome', and literature presents with only a few case reports [7,9]. Males are predominantly affected more as compared to females and commonly there is affection in the age group of 20 to 50 years with affection in children being rarely reported [2][3][4][5][6][7]10].…”

Section: Discussionmentioning

confidence: 99%

“…MRI of the knee joint presents with hypointense calcification and signal alterations from the low signal intensity on T1W to the high signal intensity on the T2W sequences [2,3,12]. MRI findings are based on the mineralization status to present various calcifications [7]. The differential diagnosis includes rheumatoid arthritis, psoriatic arthritis, inflammatory arthritis, tumoral calcinosis, villous nodular synovitis, synovial chondrosarcoma, and lipoma arborescence [9,10].…”

Section: Discussionmentioning

confidence: 99%

“…Radiology can be more expressive in its initial presentation as subtle calcifications in and around the knee joint, either intra-articular or extra-articular, can be seen [ 2 ]. Intraarticular lesions form in 70 to 95% of cases, and extraarticular loose bodies form in 20% to 50% of affections [ 7 ]. However, lack of calcification in nodules during the early stages of presentation may cause 30% of the cases likely to be missed in the initial stages [ 4 , 10 ].…”

Section: Discussionmentioning

confidence: 99%

“…Such an uncommon etiology poses diagnostic and management dilemmas. The literature review presented a few case reports of PSC affecting the knee joint as rare presentations [3,[5][6][7]. Arthroscopic synovectomy has given good functional outcomes.…”

Section: Introductionmentioning

confidence: 99%

See 4 more Smart Citations

Synovial Chondromatosis-Induced Monoarticular Knee Arthritis: Challenges With Arthroscopic Synovectomy on Late Presentation

Tomar¹,

Arya²,

Govil³

et al. 2022

Cureus

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Unilateral painful swelling of the knee is one of the most common orthopedic presentations. Monoarticular synovitis of the knee may be present due to inflammation, trauma, age-related degeneration, or tumor pathology. Primary synovial chondromatosis (PSC) is an uncommon cause.A 40-year-old female presented with painful swelling of her left knee for around nine months. She had a flexion deformity of her left knee with minimal hydrops. The radiograph showed speckled calcifications and osteopenia with a reduction of medial joint space. MRI imaging confirmed synovitis with calcifications. She underwent an arthroscopic synovectomy for her management. Her biopsy was consistent with synovial chondromatosis. The initial progression was favorable to allowing independent, unsupported, pain-free activities of daily routine. At three months, however, there was disease progression, causing limitation of knee movements and the need for a walker for support.An uncommon cause of synovitis presents at a late stage with a delay in the early diagnosis and early recognition. PSC is considered a benign lesion with good functional outcomes after arthroscopic surgery. Recurrence and poor functional outcome possibly suggest aggressive disease.A delayed diagnosis and late presentation may be susceptible to recurrence and poor functional outcome, even after an adequate arthroscopic debridement and rigorous post-operative rehabilitation program.

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