Progesterone Treatment Experience in a Patient with Lymphangioleiomyomatosis Presenting with Recurrent Pneumothorax

Abstract

Lymphangioleiomyomatosis (LAM) is a rare interstitial lung disease. Patients with LAM generally present with dyspnea and spontaneous pneumothorax. Today, while there is no proven medical treatment method for LAM, progesterone is among the widely used drugs. In this report, the effect of approximately 1 year of progesterone treatment in a patient with LAM, presenting with recurrent pneumothorax, was evaluated.