Prognosis in Endocardial Fibroelastosis

Linde, Leonard M.; Adams, Forrest H.

doi:10.1001/archpedi.1963.02080040331002

Cited by 7 publications

(8 citation statements)

References 16 publications

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“…Among the patients who died, nine out of ten examined had an increased pressure in the pulmonary artery, whereas the group of survivors comprises only one patient out of seven examined with increased pressure. The same tendency is observed in the material of Linde and Adams (11).…”

Section: Discussionsupporting

confidence: 83%

“…At right heart catheterization including pressure measurements, normal pressure as well as increased pressure in the pulmonary artery have been found in cases of endocardial fibroelastosis (8,11). We have made similar observations.…”

Section: Discussionsupporting

confidence: 81%

“…In the great majority of cases the cardiac symptoms of endo cardial fibroelastosis set in during the first six months of life (1,11). In our series the symptoms occurred within the first six months of life in 15 out of the 18 patients, and in one patient only the symptoms occurred late in the second year of life.…”

Section: Discussionmentioning

confidence: 49%

“…The angiocardiographic pattern with a very slight change in volume between systole and diastole and slow emptying of con trast medium from the left auricle and/or the left ventricle is typical for endocardial fibroelastosis (8,11), although it is not specific, since the same pattern can be seen, e.g., in myocarditis (12). Hence, the diagnosis of primary endocardial fibroelastosis cannot be made exclusively on the basis of the angiocardiographic finding, although this finding may support the diagnosis con siderably.…”

Section: Discussionmentioning

confidence: 99%

“…but ranges below 10% of all children with congenital heart diseases. Previously the prognosis was considered to be extremely poor (3), but to-day it seems to have improved after the introduction of digitalis (11,13). Consequently, it is of vital importance to be able to reach a diagnosis of the condition as early as possible, and according to Sellers et al (19) the majority of cases can be diagnosed on the following criteria: onset of congestive heart failure under 2 years of age: absence of organic heart murmurs: electrocardiographic evidence of left ventricular overloading; and abnormal T waves in leads Vs and Vo.…”

mentioning

confidence: 99%

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Primary Endocardial Fibroelastosis

Vestermark¹

1966

Cardiology

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Section: Discussionsupporting

confidence: 83%

Section: Discussionsupporting

confidence: 81%

Section: Discussionmentioning

confidence: 49%

Section: Discussionmentioning

confidence: 99%

mentioning

confidence: 99%

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Primary Endocardial Fibroelastosis

Vestermark¹

1966

Cardiology

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Atrial Fibrillation in Endocardial Fibroelastosis

Ainger¹

1966

Am J Dis Child

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ALTHOUGH current evidence is somewhat contradictory, there is reason to believe that restoration of a normal sinus rhythm and the atrial transport function in patients with atrial fibrillation will shift the ventricular function curve to an area of improved performance.1 Atrial fibrillation, a common arrhythmia in adults, is encountered infrequently in infants and children. This probably reflects the relative rarity of mitral valvular disease during this period of life. Atrial fibrillation has been related to prolonged pressure or volume distention of the atria.2The purpose of this report is to describe the clinical course of an infant with endocardial fibroelastosis with mitral insufficiency and mild aortic regurgitation demonstrated during life by left ventricular angiography and retrograde aortography, respectively. He developed atrial fibrillation approximately five weeks before death. Normal sinus rhythm was restored by synchronized direct current countershock, and the patient was given diphenylhydantoin (Dilantin) as an antiarrhythmic agent. A normal sinus mechanism persisted until a few hours prior to his death one month later. Case ReportA 9-month-old white male infant was evaluated for the first time at this center on April 23, 1965.He had just been discharged from his local com¬ munity hospital where he had been treated for con¬ gestive heart failure which was of a one-week duration and iron deficiency anemia. The referring physician's diagnosis was endocardial fibroelastosis ; there was a positive mumps skin-antigen test as described by Noren et al.3 He was receiving a main¬ tenance dose of digoxin (Elixir of Lanoxin), 0.0375 mg twice a day, and an oral iron preparation for his anemia.He was a 21-year-old mother's third child. Her pregnancy had been uneventful, and delivery oc¬ curred at term. The infant's birth weight was 7 lb 8 oz (3,402 gm). The neonatal coarse was not re¬ markable, and the child was apparently growing and developing normally until the onset of the pres¬ ent illness.A female sibling, evaluated at this clinic two years previously, had died at the age of 14 months ; the clinical diagnosis of endocardial fibroelastosis had been confirmed by postmortem examination. An electrocardiogram obtained just prior to death showed atrial fibrillation.Physical Examination.-Although the infant was pale, he appeared well nourished. He was mildly dyspneic at rest. His weight was 17 lb and 2 oz (7,767.76 gm) ; length, 27.5 inches (70 cm). Blood pressures were 89/60 and 100/60 mm Hg in the arms and legs, respectively. Pulse rate was 120 beats per minute and respiratory rate, during light sleep, was 34/minute. Abnormal physical findings were confined to the chest and abdomen. The lungs were clear to auscul¬ tation and normal to percussion. The cardiac apical impulse was in the fifth left interspace in the an¬ terior axillary line and was characterized by a sus¬ tained systolic heave. No thrills were felt over the precordium. Heart sounds were faint and distant, particularly the first heart sound at the ...

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Coarctation Of the Aorta

Margileth¹

1964

Arch Surg

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Prognosis in Endocardial Fibroelastosis

Cited by 7 publications

References 16 publications

Primary Endocardial Fibroelastosis

Primary Endocardial Fibroelastosis

Atrial Fibrillation in Endocardial Fibroelastosis

Coarctation Of the Aorta

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