Proximal Absence of the Right Pulmonary Artery in the Adult

Fj, Catala; Martí-Bonmatí, L; Morales-Marin, P

doi:10.1097/00005382-199322000-00010

Cited by 20 publications

(1 citation statement)

References 0 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…In patients with unilateral pulmonary artery agenesis (UPAA), intrapulmonary vessels and the distal portion of the affected pulmonary artery trunk often develop normally and usually receive their blood supply by systemic collaterals from bronchial, intercostal, subclavian, or subdiaphragmatic arteries [10, 11]. These collaterals enter the lungs and supply the segmental pulmonary arteries.…”

Section: Discussionmentioning

confidence: 99%

Congenital Absence of the Right Pulmonary Artery with Coronary Collaterals Supplying the Affected Lung: Effect on Coronary Perfusion

2007

View full text Add to dashboard Cite

We describe a unique case of congenital absence of a right pulmonary artery presenting in a patient of advanced age and initially misdiagnosed as coronary artery disease. Perfusion of the affected lung was accomplished via anomalous collaterals from right and left circumflex coronary arteries which induced myocardial ischemia, as demonstrated by myocardial perfusion scan. To our knowledge there are only three reports in the international literature, describing unilateral pulmonary artery agenesis with the coronary artery supplying the abnormal lung. All these reports described that the existence of such vessels does not affect the myocardial perfusion. However, here we describe, to our knowledge, for the first time that in a patient with unilateral pulmonary artery agenesis, the existence of collaterals from the coronary arteries to the affected lung can actually have a negative effect in myocardial perfusion and can induce myocardial ischemia. In conclusion, clinicians should be aware of the possibility of undiagnosed cases of unilateral pulmonary artery agenesis presenting with chest pain in advanced age.

show abstract

Section: Discussionmentioning

confidence: 99%