Prune belly syndrome: a case of early prenatal diagnosis

Abstract

Prune belly syndrome is a rare congenital disorder typically characterized by a triad of malformation of the urogenital tract, defect of abdominal wall musculature, and cryptorchidism. The condition is generally incompatible with life as infants born with this syndrome are either stillborn or die within the first few weeks of life. The present case is of a fetus presenting with prune bell syndrome, detected in first trimester of pregnancy.

A rare case: Congenital Megalourethra in prune belly syndrome

“…Prune Belly syndrome (PBS), irst described in 1839 by Frolich, is a very rare congenital abnormality [1]. It is seen in approximately 1 in 40.000 males [2].…”