Pseudopapillary solid tumor of the pancreas: case report and literature review

Abstract

Solid pseudopapillary tumor of the pancreas (NSSP) is a rare tumor entity, of unknown cause and good prognosis. It mainly affects women between 25 and 35 years of age. Occasionally, it occurs in the pediatric age group and is characterized by the presence of abdominal pain and mass. Treatment is complete surgical resection. The following clinical case of a 10-year-old girl is shared in order to report the diagnostic and therapeutic experience of this disease. The patient debuted with pain and tumor mass at abdominal level, being initially diagnosed as Wilms tumor; however, due to the lack of response to chemotherapy, it was decided to perform an exploratory laparotomy, finding a mass confined to the body and tail of the pancreas. Pathological anatomy concluded that it was a NSSP. There is little documented evidence on this disease, especially in the pediatric population, so the case is important. It is a disease with a good prognosis and low mortality after surgical treatment.