Pseudotumor cerebri associated with Sjögren's syndrome

Stanescu, Dinu; Bodaghi, Bahram; Huong, D. Lê Thi; Miléa, Dan; Goulet-Salmon, B.; Piette, Jean‐Charles; LeHoang, Phuc

doi:10.1007/s00417-002-0620-6

Cited by 9 publications

(8 citation statements)

References 19 publications

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“…Increased ICP has been noted as the initial manifestation of some systemic inflammatory disorders, including lupus, Sjogren’s syndrome, and Kawasaki disease 6 7 8 . We posit that our patients’ increased ICP similarly reflects systemic inflammation related to SARS-CoV-2 infection, resulting in central nervous system (CNS) effects.…”

Section: Discussionmentioning

confidence: 99%

Increased Intracranial Pressure in the Setting of Multisystem Inflammatory Syndrome in Children, Associated With COVID-19

Baccarella

Linder

Spencer

et al. 2021

Pediatric Neurology

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This is a PDF file of an article that has undergone enhancements after acceptance, such as the addition of a cover page and metadata, and formatting for readability, but it is not yet the definitive version of record. This version will undergo additional copyediting, typesetting and review before it is published in its final form, but we are providing this version to give early visibility of the article. Please note that, during the production process, errors may be discovered which could affect the content, and all legal disclaimers that apply to the journal pertain.

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Section: Discussionmentioning

confidence: 99%

Increased Intracranial Pressure in the Setting of Multisystem Inflammatory Syndrome in Children, Associated With COVID-19

Baccarella

Linder

Spencer

et al. 2021

Pediatric Neurology

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“…The facial nerve supplies the autonomic function of the salivary and the lacrimal glands. A few cases of Sicca syndrome94 were reported in patients with IICH. According to this hypothesis, this may be due to the compression of the autonomic fibers running toward the salivary and lacrimal glands.…”

Section: Symptoms Associated With Increased Icpmentioning

confidence: 99%

The link between idiopathic intracranial hypertension, fibromyalgia, and chronic fatigue syndrome: exploration of a shared pathophysiology

Hulens¹,

Rasschaert²,

Vansant³

et al. 2018

JPR

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PurposeIdiopathic intracranial hypertension (IICH) is a condition characterized by raised intracranial pressure (ICP), and its diagnosis is established when the opening pressure measured during a lumbar puncture is elevated >20 cm H2O in nonobese patients or >25 cm H2O in obese patients. Papilledema is caused by forced filling of the optic nerve sheath with cerebrospinal fluid (CSF). Other common but underappreciated symptoms of IICH are neck pain, back pain, and radicular pain in the arms and legs resulting from associated increased spinal pressure and forced filling of the spinal nerves with CSF. Widespread pain and also several other characteristics of IICH share notable similarities with characteristics of fibromyalgia (FM) and chronic fatigue syndrome (CFS), two overlapping chronic pain conditions. The aim of this review was to compare literature data regarding the characteristics of IICH, FM, and CFS and to link the shared data to an apparent underlying physiopathology, that is, increased ICP.MethodsData in the literature regarding these three conditions were compared and linked to the hypothesis of the shared underlying physiopathology of increased cerebrospinal pressure.ResultsThe shared characteristics of IICH, FM, and CFS that can be caused by increased ICP include headaches, fatigue, cognitive impairment, loss of gray matter, involvement of cranial nerves, and overload of the lymphatic olfactory pathway. Increased pressure in the spinal canal and in peripheral nerve root sheaths causes widespread pain, weakness in the arms and legs, walking difficulties (ataxia), and bladder, bowel, and sphincter symptoms. Additionally, IICH, FM, and CFS are frequently associated with sympathetic overactivity symptoms and obesity. These conditions share a strong female predominance and are frequently associated with Ehlers-Danlos syndrome.ConclusionIICH, FM, and CFS share a large variety of symptoms that might all be explained by the same pathophysiology of increased cerebrospinal pressure.

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“…A report has suggested that central nervous system symptoms can be the initial manifestation of pSS when mild complaints of sicca symptoms are overlooked. [ 2 ] No associated conditions linked to benign intracranial hypertension syndrome were seen in our patient. The pathophysiological mechanism of intracranial hypertension in pSS remains unknown.…”

mentioning

confidence: 74%

“…venous thrombosis, medication side effects, vasculitis, immune complex precipitation or even direct antibody injury). [ 1 2 3 4 ] This case expands the spectrum of presentation of pSS that has an important impact in the long-term timely management of such patients.…”

mentioning

confidence: 92%

“…There are only few prior reports of intracranial hypertension syndrome as the presenting symptom of primary Sjogren's syndrome (pSS). [ 1 2 ] We describe one such patient. A 38-year-old normotensive woman presented with headache of 18 months duration with increased severity since 2 months accompanied by transient visual obscurations and tinnitus in both ears.…”

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confidence: 99%

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A rare initial neurological presentation of Sjogren’s syndrome

Kumar

2015

Journal of Neurosciences in Rural Practice

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Pseudotumor cerebri associated with Sjögren's syndrome

Abstract: Sjögren's syndrome should be considered in the different etiologies of pseudotumor cerebri. The major improvement with corticosteroids and ventriculoperitoneal shunt makes prompt diagnosis essential.

Cited by 9 publications

References 19 publications

Increased Intracranial Pressure in the Setting of Multisystem Inflammatory Syndrome in Children, Associated With COVID-19

Increased Intracranial Pressure in the Setting of Multisystem Inflammatory Syndrome in Children, Associated With COVID-19

The link between idiopathic intracranial hypertension, fibromyalgia, and chronic fatigue syndrome: exploration of a shared pathophysiology

A rare initial neurological presentation of Sjogren’s syndrome

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