Behcet's disease (BD) is a rare condition in sub-Saharan Africa. It often manifests as recurrent oral and genital aphthous ulcers with ocular features and infrequently involving major systems like pulmonary vasculature and parenchyma. Pulmonary involvement in BD, although rare, can manifest as pulmonary artery aneurysm, vascular thrombosis, pulmonary infarction, pneumonia and pleurisy.Our index case is a 38 year old Nigerian who presented with recurrent orogenital ulcer, hemoptysis and uveitis. He had a contrast enhanced chest CT scan that revealed pulmonary artery aneurysm. His symptoms resolved following commencement of immunosuppressant and steroid.Increased awareness is required for early detection of BD especially in regions where it is regarded as rare. Furthermore, multidisciplinary approach in its management is vital to reduce morbidity and mortality.