Pulmonary artery aneurysm associated with a nonstenotic bicuspid pulmonic valve: A role for genetics?

Abstract

Background: Bicuspid pulmonic valves are quite uncommon, being described in only 0.1% of donor's hearts, while pulmonary artery aneurysms (PAAs) are even rarer, having been found in 8 out of 109,571 autopsies. This rarity makes it difficult to characterize the relationship between them.