Pulmonary Manifestations of Primary Sjögren's Syndrome

Abstract

Among a diversity of pulmonary lesions in primary Sjogren's syndrome, NSIP was the commonest histologic pattern and had a favorable prognosis.

A Case of Lung Involvement Showing Multiple Lung Cysts in Primary Sjögren's Syndrome

“…, 46% of patients with Sjögren's syndrome showed obstructive disease. However, most studies reported higher incidences of restrictive disease 2,5 . Small airway narrowing and obstructive lung disease are thought to be related to peribronchiolar lymphocytic infiltration 10,11 .…”

Sjoegren's Syndrome with Multiple Cystic Lesions and Pulmonary Arteriovenous Fistulae

“…In previous studies, about 10% of Sjögren's syndrome patients have cystic lesions in their lungs (2,3). In addition, some cases of complicating pulmonary multiple cystic lesions have been reported (2,(4)(5)(6)(7)(8)(9).…”

“…In addition, some cases of complicating pulmonary multiple cystic lesions have been reported (2,(4)(5)(6)(7)(8)(9). They are complicated with amyloidosis (4)(5)(6), malignant lymphoma (2) and lymphocytic interstitial pneumonia (8,9).…”

“…In addition, some cases of complicating pulmonary multiple cystic lesions have been reported (2,(4)(5)(6)(7)(8)(9). They are complicated with amyloidosis (4)(5)(6), malignant lymphoma (2) and lymphocytic interstitial pneumonia (8,9). The process of the formation of cystic lesions is regarded as a ball-valve mechanism with stenosis of the bronchioli and fragile alveolar walls due to severe infiltration of inflammatory cells (6,7) or amyloid deposits (4)(5)(6) Hi s t o l o g i c a l f i n d i n g s o f t h e p u l mo n a r y a r t e r i o v e n o u s f i s t u l a e s h o we d a n a g g r e g a t e o f v e i n s a n d a r t e r i e s a r o u n d t h e b r o n c h i a n d b r o n c h i o l e …”

Organizing pneumonia associated with Sjogren’s syndrome: a comment

“…They concluded by a pathologic study that non-speciWc interstitial pneumonitis (NSIP) is the commonest form of interstitial lung disease caused by Sjogren's syndrome [3]. However, it is not appropriate to make such a conclusion according to the current evidence.…”