Pulseless Disease a Report on Five Cases

Dermatitis Gangrenosa Infantum Leading to Supravalvular Aortic Stenosis (Aortic Arch Syndrome)

“…Koszewski & Hubbard (1957) reported a case in a 13-year-old negress who had an acute neutrophilic arteritis and thrombosis in which the adventitia was infiltrated by lymphocytes and plasma cells. Caldwell & Skipper (1961) recorded 5 cases of pulseless disease seen in Sheffield since 1948; all were adults, 3 of whom had nonspecific arteritis. One, a woman of 37, was found to have moderate coarctation of the aorta as well as scarring and constriction of the mouths of the vessels leading from the aortic arch.…”