Pyoderma gangrenosum in a patient with lipoid proteinosis (Urbach–Wiethe disease)

A Sporadic Family of Lipoid Proteinosis with Novel ECM1 Gene Mutations

“… 3 , 10 , 11 There have been reports of disabling tongue ulcers developing among LP patients, which improve following oral corticosteroid treatment, resulting in gradual epithelization of the ulcer. 12 …”

“…3,10,11 There have been reports of disabling tongue ulcers developing among LP patients, which improve following oral corticosteroid treatment, resulting in gradual epithelization of the ulcer. 12 LP is frequently observed in offspring of consanguineous marriages. A study revealed that 20% of LP probands' parents were from consanguineous unions.…”