Rare Association Between Atrioventricular Septal Defect and Partial Anomalous Pulmonary Venous Connection

Abstract

Clinical dataInfant, 7 months, female, referred to our department at one month of age, suspecting of congenital heart disease for further investigation.Chest radiographyDemonstrates cardiomegaly and prominent pulmonary vascular markings.ElectrocardiographyShows right ventricular hypertrophy and left anterior fascicular block.EchocardiographyEvidenced common atrioventricular valve with two orifices and the left superior pulmonary vein draining on the brachiocephalic vein.Computed tomography angiographyThis complementary imaging exam was performed to confirm the diagnosis.DiagnosisThe patient presented an association between AVSD and PAPVC, a rare combination. The clinical picture of heart failure was preponderant, characterized by need for diuretics and complementary exams findings, and early surgical treatment was indicated.OperationThe operation was performed through a median sternotomy with 123 minutes of cardiopulmonary bypass and 89 minutes of cross-clamping time. The patient had no postoperative complications, remaining 10 days hospitalized.