Rare case of Budd-Chiari Syndrome with recurrent thrombosis requiring stenting

Abstract

Budd-Chiari syndrome is a very rare disorder in paediatric age group, which is characterised by narrowing or obstruction of hepatic venous outflow. The obstruction might be thrombotic or non-thrombotic along the course of hepatic venules to junction of inferior vena cava to the right atrium, which leads to abdominal pain in right hypochondrium, hepatomegaly, ascites and portal hypertension. The cause of venous obstruction in children is mainly due to hypercoagulable state. The mean age of Budd-Chiari syndrome is 20-40 years, but here we can see that it occurs in paediatric age group, so good clinical suspicion is required along with investigation to confirm the diagnosis. Traditional approach to the treatment of Budd-Chiari syndrome is systemic thrombolysis or surgical Porto systemic shunt. Recently, successful treatment of Budd-Chiari syndrome is done by endovascular techniques, including angioplasty and stent placement. Here, in this case it shows a successful percutaneous recanalization of complete hepatic vein occlusion by angioplasty and stent placement.