Rare cause of fatal acute abdomen-celiac artery aneurysm

Rajahram, Dhadchayini; Satchithanantham, Vinojan; Veerasingam, Suthagaran; Tharmalingam, Thulasi

doi:10.1016/j.ijscr.2023.108546

Cited by 1 publication

(1 citation statement)

References 12 publications

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“…In contrast, in a report examining 40 aneurysm lesions associated with NF1, there were only two cases involving the liver artery, one case involving the gastroduodenal artery, and one case involving the pancreaticoduodenal artery, indicating that abdominal visceral aneurysms are rare [ 9 ]. There have been several reports of abdominal visceral aneurysms associated with NF1, including liver, superior mesenteric, inferior mesenteric, celiac, gastroduodenal, and superior rectal arteries [ 4 – 6 , 9 , 19 – 34 ] (Table 1 ). However, to our knowledge, there are no reports of splenic aneurysms associated with NF1 in the relevant English literature, and we believe that this is the first report of such an aneurysm.…”

Section: Discussionmentioning

confidence: 99%

Robotic resection for splenic artery aneurysm associated with neurofibromatosis type 1: a case report

Ueda,

Saito,

Murase

et al. 2024

J Med Case Reports

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Background Neurofibromatosis type 1 is an autosomal-dominant disease characterized by café-au-lait spots and neurofibromas, as well as various other symptoms in the bones, eyes, and nervous system. Due to its connection with vascular fragility, neurofibromatosis type 1 has been reported to be associated with vascular lesions, such as aneurysms. However, there have been few reports of abdominal visceral aneurysms associated with neurofibromatosis type 1. Furthermore, there have been no reports of robotic treatment of aneurysms associated with neurofibromatosis type 1. In this report, we describe the case of a patient with neurofibromatosis type 1 with a splenic artery aneurysm who was successfully treated with robotic surgery. Case presentation This report describes a 41-year-old Asian woman with a history of neurofibromatosis type 1 who was referred to our hospital for evaluation of a 28 mm splenic artery aneurysm observed on abdominal ultrasound. The aneurysm was in the splenic hilum, and transcatheter arterial embolization was attempted; however, this was difficult due to the tortuosity of the splenic artery. Thus, we suggested minimally invasive robotic surgery for treatment and resection of the splenic artery aneurysm with preservation of the spleen. The postoperative course was uneventful, and the patient was discharged on the eighth day after surgery. At 1 year of follow-up, the patient was doing well, with no evidence of recurrence. Conclusion We encountered a rare case of splenic artery aneurysm in a patient with neurofibromatosis type 1 who was successfully treated with robotic surgery. There is no consensus on treatment modalities for neurofibromatosis-related aneurysms, and endovascular treatment is considered safe and effective; however, surgery remains an important treatment modality. Especially in patients with stable hemodynamic status, robotic surgery may be considered as definitive treatment. To our knowledge, this is the first successfully treated case of a splenic artery aneurysm in a patient with neurofibromatosis type 1.

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