Rare cause of haemoptysis: bronchopulmonary sequestration

Abstract

Bronchopulmonary sequestration is a rare congenital pulmonary abnormality of the lower airways, which includes an abnormal and non-functioning lung tissue not communicating with the tracheobronchial tree and having aberrant blood supply from systemic circulation with variable venous drainage. The incidence of sequestration is around 0.15%–6.4% of all congenital lung malformations.Common presenting features are cough and expectoration. Misdiagnosed cases may present with recurrent infections and haemoptysis. CT of the chest with contrast is the imaging modality of choice.This is a case report of a 32-year-old woman who presented with cough and haemoptysis. CT of the chest showed a multiloculated mass-like lesion in the left lower lobe with a feeding artery from coeliac plexus and venous drainage via the normal left pulmonary vein.Based on CT chest findings, diagnosis of intralobar pulmonary sequestration was made. The patient was reviewed by cardiothoracic surgeons and underwent surgical resection of the sequestrated lung.Common presenting features are cough and expectoration. Misdiagnosed cases may present with recurrent infections and haemoptysis. CT of the chest with contrast is the imaging modality of choice.

Rare presentation of pneumothorax in a young woman with underlying congenital pulmonary airway malformation

“…CPAM can be differentiated from BPS as it receives its blood supply from the pulmonary circulation. In contrast, BPS has a systemic arterial supply and does not have a connection with the tracheobronchial tree 4 5. The macroscopic examination of the surgical specimen in our case did not reveal any feeding vessel from systemic circulation, which ruled out BPS.…”

Right upper lobe pulmonary sequestration masquerading clinically and radiologically as malignancy: a case report

“…Some authors argue that a ‘wait-and-watch’ approach may be used for asymptomatic patients; however, this is an area of contention [ 8 , 9 ]. Certainly, there are reports of patients developing complications of BPS such as infection and abscess formation; yet, perhaps most pertinently, there are numerous documented cases of near-fatal haemoptysis and one case ending in fatal haemoptysis [ 10–12 ].…”

Rare case of bilateral bronchopulmonary sequestration

“…Respiratory symptoms including persistent cough and expectoration after birth are uncommon, but when present, typically occur in conjunction with larger BPS lesions, hydrothorax, or hydrops. When misdiagnosed or undiagnosed, cases may present with recurrent infections and hemoptysis [10] . As mentioned earlier regarding the anatomy, interlobar BPS in particular carries an increased risk for infection.…”

“…Symptomatic cases are treated surgically [5] . This classically involves surgical resection of sequestrated segments [10] . Embolization and radiofrequency ablation of the feeding systemic artery have also been explored as 2 other potential surgical strategies [ 11 , 12 ].…”