Rare presentation of essential lingual myoclonus

Lingual epilepsia partialis continua: a detailed video‐EEG and neuroimaging study

“…Clinically, an isolated non‐epileptic lingual myoclonus should be included in the differential diagnosis in these cases. We can distinguish two types of non‐epileptic lingual myoclonus: one that is secondary to a lesion of the nervous system (symptomatic lingual myoclonus), most likely due to brainstem damage in the context of Arnold‐Chiari malformation, pontine traumatism or hypoxia, and another in which a specific cause is not found which is called “essential lingual myoclonus” (Bettoni et al ., 1999; Patel and Tappuni, 2018). Obviously, the use of v‐EEG and brain MRI are necessary for reaching an accurate diagnosis.…”

Lingual and Facial Myoclonus Associated with Early Corticobasal Syndrome

“…Lingual myoclonus is itself a very rare phenomenon, to date described sporadically as either a primary essential phenomenon, often rhythmic, 8 , 9 or as a secondary phenomenon, including various cortical and subcortical causes. 10 , 11 , 12 The lack of response to antiseizure medications in our case is noteworthy, as previously reported cases of lingual myoclonus of other etiologies have responded at least in part to, for example, clonazepam, 8 , 12 valproate, 9 lacosamide, levetiracetam, phenytoin, 10 and topiramate. 11 …”