To describe the presentation of a pulmonary artery dissection to the Emergency Unit, the sequence of events, and a literature review. Case report: A 59-year-old female patient with known Chagas heart disease presented at the Emergency Unit with an event of sudden, stabbing chest pain and progressive dyspnea, evolving rapidly to cardiogenic shock. A chest radiograph reported severe widening of the mediastinum and cardiomegaly; therefore, a thoracic angiotomography was performed to rule out acute aortic syndrome, in which a dissecting pulmonary artery aneurysm was diagnosed. Transthoracic echocardiogram showed an intimal flap at the pulmonary artery and severe dilatation. The patient died in less than four hours after arrival at the emergency room without being able to access surgical treatment due to the rapid evolution. Conclusion: Pulmonary artery dissection is a rare disease, with a high rate of mortality. Optimal management requires a rapid diagnosis with multiple imaging techniques. There is a lack of information about this topic.