Rectal hemangiopericytoma in a 37-year-old woman: a case report and review of the literature

Abstract

IntroductionHemangiopericytoma is an uncommon perivascular tumor. Rectal Hemangiopericytomas are extremely rare. To the best of our knowledge, only two cases have been reported in the literature.Case presentationWe report the case of a 37-year-old Asian woman with an Hemangiopericytoma rising from the anterior wall of her rectum. Abdominopelvic computed tomography showed a 7.4 cm solid mass between her uterus and her rectum. Heterogeneous gradual enhancement after intravenous injection of contrast material was noted with several tortuous vessels around her tumor. Intra-operative findings indicated a capsule and well-circumscribed solid tumor connecting with the anterior wall of her rectum by a small pedicle. With immunohistochemical stains, her tumor cells reacted positive for Bcl-2, CD34, and ki67 and negative for CD10, CD117, S100, and Desmin. Follow-up computed tomography scans have shown no tumor recurrence or metastasis signs.ConclusionsRectal Hemangiopericytoma is a rare tumor with non-specific imaging findings. Hemangiopericytomas should be included in the differential list when a massive tumor with heterogeneously gradual enhancement in the regions of the rectum is encountered.

Multidisciplinary Management of Metastatic Hemangiopericytoma Presenting with Hypoglycemia

“…Overall 5-year survival rates for localized disease treated with complete resection of the primary tumor are reported to be between 71% and 86% [6][7][8] with 5-year recurrence rates of up to 65% for tumors arising from the meninges [9]. The most common sites of metastatic disease are bone, liver, and lung [10]. Complete surgical resection is the mainstay of treatment for HPC.…”