Recurrent cutaneous angiosarcoma of the ear masquerading as atypical fibroxanthoma

González, Catalina; Hawkes, Jason E.; Bowles, Tawnya L.

doi:10.1016/j.jdcr.2016.09.005

Cited by 3 publications

(1 citation statement)

References 9 publications

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“…Fifty percent of all angiosarcomas involve the skin of the head and neck, whereas auricular involvement is very rare. To our knowledge, only 7 cases of auricular angiosarcoma, including the present case, have been reported (Table 1 ) [ 2 , 3 , 4 , 5 , 6 , 7 ]. The patients comprised 4 males and 3 females, with a wide age range (31–90 years).…”

Section: Discussionmentioning

confidence: 99%

Angiosarcoma of the Auricle in a Patient with Xeroderma Pigmentosum Variant

et al. 2020

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Xeroderma pigmentosum (XP) is an inherited autosomal recessive disorder characterized by photosensitivity and an increased risk of developing multiple skin neoplasms at sites exposed to the sun. We report a 73-year-old Japanese man with angiosarcoma of the auricle and an XP-variant, which is a very rare condition. In this case, long-term physical stimulation due to auricular deformation after surgery may have been the cause. Angiosarcoma associated with XP has a better prognosis than common angiosarcoma, perhaps because of the smaller tumor size. As XP patients are at high risk of skin neoplasms, they consult dermatologists regularly, and therefore skin tumors are likely to be detected early.

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Section: Discussionmentioning

confidence: 99%

Angiosarcoma of the Auricle in a Patient with Xeroderma Pigmentosum Variant

et al. 2020

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Cutaneous angiosarcoma: a current update

et al. 2017

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Cutaneous angiosarcoma (cAS) is a rare malignant neoplasm with variable clinical presentation. Although a distinct vascular tumour, cAS shares many overlapping histopathological features with other vasoformative and epithelioid tumours or 'mimickers'. cAS shows aggressive behaviour and carries a grave prognosis, thus early diagnosis is of paramount importance to achieve the best possible outcomes. Recently, several genetic studies were conducted leading to the identification of novel molecular targets in the treatment of cAS. Herein, we present a comprehensive review of cAS with discussion of its clinical, histopathological and molecular aspects, the differential diagnosis, as well as current therapies including ongoing clinical trials.

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