Recurrent Haemoptysis Revealing Hughes-Stovin Syndrome

Moussa, N.; Znegui, Tasnim; Snoussi, M.; Gargouri, R.; Bahloul, Z.; Abid, S.; Kammoun, S.

doi:10.12890/2021_002810

Cited by 3 publications

(7 citation statements)

References 11 publications

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“…Typical manifestations of this syndrome are cough, shortness of breath, fever, and chest pain [ 57 ]. As BD, HSS may present with hemoptysis [ 58 ]. As for PAAs, steroid therapy associated or not with immunosuppressants has been suggested [ 59 , 60 ].…”

Section: Imaging Approach To Thoracic Involvement In Behcet’s Diseasementioning

confidence: 99%

Behçet’s Disease: A Radiological Review of Vascular and Parenchymal Pulmonary Involvement

et al. 2022

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Behcet’s disease (BD) is a chronic systemic inflammatory disorder characterized by underlying chronic vasculitis of both large- and small-caliber vessels. Thoracic involvement in BD can occur with various types of manifestations, which can be detected with contrast-enhanced MSCT scanning. In addition, MR can be useful in diagnosis. Characteristic features are aneurysms of the pulmonary arteries that can cause severe hemoptysis and SVC thrombosis that manifests as SVC syndrome. Other manifestations are aortic and bronchial artery aneurysms, alveolar hemorrhage, pulmonary infarction, and rarely pleural effusion. Achieving the right diagnosis of these manifestations is important for setting the correct therapy and improving the patient’s outcome.

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Section: Imaging Approach To Thoracic Involvement In Behcet’s Diseasementioning

confidence: 99%

Behçet’s Disease: A Radiological Review of Vascular and Parenchymal Pulmonary Involvement

et al. 2022

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“…Although the first descriptions as well as the definition of the disease state that aneurysms are located in the pulmonary or the bronchial arteries, aneurysms can occur anywhere in the arterial system, as they have been described in the external carotid, iliac artery, left hepatic artery and in the ascending aorta [ 9 , 18 – 20 ].…”

Section: Disease Descriptionmentioning

confidence: 99%

“…A differential diagnosis of HSS is Behçet’s disease (BD), as both of them can present with thrombosis and pulmonary aneurysms. In many published reports we believe that HSS is an incomplete form of BD or a cardio- vascular manifestation of BD as there in an overlap between clinical, radiological and histological findings between BD and HSS [ 20 , 22 , 32 , 33 ].…”

Section: Differential Diagnosismentioning

confidence: 99%

Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome

Kéchida¹,

Daadaa²,

Jomaa³

2022

Reumatologia

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Hughes-Stovin syndrome is a rare disease characterized by thrombophlebitis associated with arterial or bronchial aneurysms. Even though it was described first in 1911, it is scarcely reported in the literature. Hughes-Stovin syndrome diagnosis is based on clinical manifestations as well as radiological findings. There are no validated criteria or specific laboratory findings to confirm the diagnosis. Computed tomography pulmonary angiography remains the gold standard for the diagnosis and follow-up of radiological findings, as they were recently described in a critical analysis of the largest cohort in the literature. The aim of this review is to draw attention to this rare but potentially fatal disease and to discuss its therapeutic options.

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“…Los aneurismas pueden ser únicos, múltiples, uni o bilaterales. La presentación clínica típica del síndrome de Hughes Stovin se relaciona con ambas situaciones 2 .…”

Section: Discussionunclassified

“…Es una enfermedad de baja frecuencia, de difícil diagnóstico y con implicancias serias por el riesgo de mortalidad debido a la ruptura de aneurismas, además por afectar a adultos jóve-nes 1 . Algunos autores consideran el síndrome de Hughes Stovin como una variante de la enfermedad de Behçet, vasculitis multisistémica que afecta a vasos de cualquier calibre 2,3,4 .…”

Section: Introductionunclassified

Aneurismas de las arterias pulmonares en relación al síndrome de Hughes Stovin

Abdala¹,

Baroni²,

Castelli³

et al. 2023

Rev. Argent. Reumatol.

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El síndrome de Hughes Stovin es una vasculitis de pequeños y grandes vasos, más frecuente en hombres jóvenes. Se manifiesta con trombosis y aneurismas. Inicia con tromboflebitis que evoluciona a aneurismas con eventual desenlace fatal por ruptura de los mismos. Algunos autores consideran el síndrome de Hughes Stovin como una variante de la enfermedad de Behçet. El diagnóstico es clínico y el tratamiento de primera línea son los corticoides y la ciclofosfamida. Frente a un caso de trombosis, la anticoagulación es controversial por el riesgo de sangrado. Presentamos el caso de un varón joven con cuadro clínico compatible en el cual se descartaron otras patologías con requerimiento de tratamiento quirúrgico por mala evolución clínica.

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Recurrent Haemoptysis Revealing Hughes-Stovin Syndrome

Abstract: Hughes-Stovin syndrome is a very rare condition with no defined diagnostic criteria. We present the case of a 26-year-old man who had haemoptysis revealing Hughes-Stovin syndrome. We will consider the aetiology, therapeutic and evolutionary aspects of this disease.

Cited by 3 publications

References 11 publications

Behçet’s Disease: A Radiological Review of Vascular and Parenchymal Pulmonary Involvement

Behçet’s Disease: A Radiological Review of Vascular and Parenchymal Pulmonary Involvement

Clinical presentation, radiological findings and treatment options in Hughes-Stovin syndrome

Aneurismas de las arterias pulmonares en relación al síndrome de Hughes Stovin

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