Recurrent Lower Respiratory Tract Infections Due to Mounier-Kuhn Syndrome

Abstract

Mounier-Kuhn syndrome (MKS) is a rare disorder characterized by recurrent lower respiratory tract infections and bronchiectasis due to dilation of the trachea and bronchi. Diagnosis is made based on clinical suspicion along with radiographic evidence of tracheobronchomegaly. Mucolytic agents and chest physiotherapy have been shown to offer symptomatic improvement, and definitive surgical treatment is reserved for those with persistent symptoms. Herein, we report a case of MKS in a 72-year-old woman with bronchiectasis and recurrent multidrug-resistant lower respiratory tract infections.

Unexpected curious cause of serious air leakage after endotracheal intubation: A case report of tracheobronchomegaly and literature review

“…Except for congenital TBM, some other clinical conditions were also associated with secondary airway enlargement; thus, the change of this patient was suspected acquired because of no congenital respiratory disease but ankylosing spondylitis. Although clinical presentations of TBM are not specific, recurrent pulmonary infection is the most common symptom ( 6 , 8 , 9 ). This is the reason why most cases of TBM were reported with the presentation of pulmonary diseases.…”

CT scan Diagnosis of Mounier-Kuhn Syndrome in A Patient with Recurrent Respiratory Infections: About A Rare Case Report

“…While tracheal stenting has been beneficial in severe cases, surgery is rarely considered given the diffuse nature of the disease. Lung transplantation has not demonstrated any benefits regarding the risk of major morbidity and death [12]. The condition can be tolerated for a long time but the evolution towards chronic respiratory failure is inevitable.…”