Rehabilitation in Patients Diagnosed with Arthrogryposis Multiplex Congenita: A Systematic Review

Abstract

Arthrogryposis multiplex congenita is a condition characterised by contractures and deformity in two or more body areas. Physiotherapy may be an appropriate treatment. The aim was to systematically review the evidence for rehabilitation in arthrogryposis multiplex congenita. A systematic review was performed following the PRISMA 2020 criteria. The search was conducted in PubMed, ScienceDirect, Scielo, Scopus, Web of Science, ENFISPO, JSTOR, Google Scholar, ProQuest, Cochrane Library and PEDro from inception until October 2022. To assess the methodological quality, we used the different aspects of the critical appraisal tool JBI. We included 14 studies (6 case reports, 5 case series, 2 cross-sectional and 1 qualitative study). Sample sizes ranged from 1 to 50 participants, with an age range between 11 days and 35 years. Most studies employed multicomponent therapy, mainly kinesitherapy, massage therapy, use of physical agents and stretching, some combined it with orthopaedic therapy, or it was complementary to surgical treatment. The key to improving the clinical picture was early and individualised care, tailored to the characteristics of the patients. Regarding methodological quality, the main conflicts encountered were in the reporting of participant characteristics and experimental interventions. Rehabilitation provides satisfactory results in the treatment of arthrogryposis multiplex congenita. More scientific production and randomised clinical trials are needed.

A Case Report: Can Prioritizing Sensory Integration Therapy Help Improve Gross Motor Function in a Rare Case of Neurogenic Arthrogryposis Multiplex Congenita?

“…In the above case, a multidisciplinary approach for rehabilitation from pediatricians, pediatric orthopedic surgeons, urologists, and physiotherapists was utilized, out of which physiotherapy treatment remained the primary focus. As per a systematic review published by García Aguilar CE et al, rehabilitation primarily by physiotherapy helps to prevent the worsening of symptoms and makes the patient functionally independent [ 11 ]. As per the study presented by Lane SJ et al, sensory integration theory acts as a catalyst for development as it focuses on active, dynamic sensory-motor processes that support movement and interaction within the social and physical environment [ 12 ].…”

Utilización De Oxígeno a Alto Flujo en Pacientes Con Insuficiencia Respiratoria Aguda en Urgencias

“…▷ RSI -Revista Sanitaria de Investigación. 2023 [citado el 22 de mayo de 2023]. Disponible en: https://revistasanitariadeinvestigacion.com/ complicaciones-mecanicas-en-los-pacientes-con-dialisis-peritoneal/.…”