Ameloblastoma is a significant tumor originating from tissue known for its aggressive nature and tendency to come back after treatment. This review explores the aspects of factors that affect prognosis and strategies for managing a rare tumor that originates from tooth related tissues. Examining patients and utilizing imaging techniques to detect the tumor at an early stage is crucial for good survivability. Prognosis is influenced by recurrence rates, types of tissue characteristics observed under a microscope and how treatments affect surrounding structures, highlighting the necessity for management approaches. Surgical removal is considered the intervention in ameloblastoma management. Histopathological examination remains the gold standard for confirming the diagnosis. Incisional biopsies are often performed to confirm the diagnosis and determine the subtype based on characteristics. Furthermore, it discusses techniques for reconstructing affected areas. Explores the benefits of additional therapies to provide a comprehensive understanding of treatment options. Managing this tumor requires considering both the psychosocial implications and the need for lifelong follow-up. As research progresses, there is potential for markers and evolving treatment methods to enhance accuracy and improve the effectiveness of treatments.