~iiigioi;i~oIiboiiiii is 11 briii$giz tuiitorw of the hidiiry, crssociated iiz iirost iiistairces zuitlz tubwozrs 'srlcrosis. O;t occasions, 110 stigmata of tuberous sclerosis coil be detectrd, and this gror~b o f aiigiont~o1iponrii.s Itas certaiii distinguishing featzirrs zvhirh are discussed w i t h a review of ihc litemttirc.. A rirtlzer i~iizisiicil case is reported, and a plea is nzcidc f o r roirscrvntisi;r i l l the surgery of these tiiittoiws.