Renal epithelioid angiomyolipoma: 2 Cases report

Boudaouara, Ons; Kallel, Rim; Smaoui, W.; Makni, S.; Mhiri, Mohamed Nabil; Mnif, H.; Boudaouara, Tahia

doi:10.1016/j.afju.2016.10.002

Cited by 2 publications

(3 citation statements)

References 8 publications

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“…6 They are composed of varying degrees of adipose tissue, muscle and blood vessels. 3,5,7 Renal AMLs (RAMLs) may be the result of a sporadic event, or may be associated with tuberous sclerosis. 7 They may also be associated with sporadic lymphangioleiomyomatosis.…”

Section: Introductionmentioning

confidence: 99%

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Embolization of Ruptured Renal Angiomyolipoma in Puerpera

Góes

Jeha

Oliveira

et al. 2019

Rev Bras Ginecol Obstet

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Angiomyolipomas (AMLs) are rare benign tumors derived from mesenchymal tissue and composed of varying degrees of adipose tissue, muscle and blood vessels. Renal AMLs (RAMLs) are the result of a sporadic event, and, in most of cases, the diagnosis is usually incidental, but hemorrhage and shock may be present. During pregnancy, the size of AMLs may increase and they may rupture, probably due to the high expression of hormone receptors, and the increase in maternal circulation and abdominal pressure. The authors present a case of a woman with ruptured RAML submitted to urgent endovascular treatment four days after giving birth by cesarean section.

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Section: Introductionmentioning

confidence: 99%

“…Angiomyolipomas (AMLs) are rare benign tumors derived from mesenchymal tissue. 1 2 3 4 5 They are classically described in the kidneys, but they can also occur in the liver, uterine tubes, ovaries, spermatic cord, colon and palate. 6 They are composed of varying degrees of adipose tissue, muscle and blood vessels.…”

Section: Introductionmentioning

confidence: 99%

Embolization of Ruptured Renal Angiomyolipoma in Puerpera

Góes

Jeha

Oliveira

et al. 2019

Rev Bras Ginecol Obstet

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“…Radical tumor resection could be an important in the treatment of early stage disease and adjuvant radio-chemotherapy may be beneficial, however there have been very few randomized control trials to corroborate these findings. [3] Targeted therapies including imatinib, crizotinib and mammalian target of rapamycin (mTOR) inhibitors are being investigated for patients with advanced disease. [4] Clinicians should be aware of this new treatment paradigm to design better treatment protocols.…”

Section: Introductionmentioning

confidence: 99%

Case report of everolimus-induced sustained partial response in metastatic renal epithelioid angiomyolipoma

Tayal

Doval

Kamboj

et al. 2019

Turkish Journal of Urology

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Epithelioid variant of angiomyolipoma (EAML) is a newly defined entity and a close mimicker of renal cell carcinoma. There is a growing body of evidence to suggest its aggressive behavior in terms of local recurrence, metastasis and death. The treatment for this subset of patients has posed challenges for the experts. Chemotherapy plays little active role and so molecular profiling to identify genomic alterations amenable to targeted therapies has paved the way. Recently, tyrosine kinase inhibitors and mTOR inhibitors have been utilised both in adjuvant and neoadjuvant settings and have shown promising results in terms of survival. We present a case of a metastatic epithelioid angiomyolipoma treated sequentially with imatinib, crizotinib and now maintaining a sustained partial response with everolimus.

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Renal epithelioid angiomyolipoma: 2 Cases report

Cited by 2 publications

References 8 publications

Embolization of Ruptured Renal Angiomyolipoma in Puerpera

Embolization of Ruptured Renal Angiomyolipoma in Puerpera

Case report of everolimus-induced sustained partial response in metastatic renal epithelioid angiomyolipoma

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