Renal lymphangiomatosis: Imaging and management of a rare renal anomaly

Abstract

Renal lymphangiomatosis is a rare developmental malformation resulting in the development of cystic masses in the peri-pelvic or peri-renal areas. We report our experience in the management of this rare anomaly. Herein, we also describe the successful laparoscopic ablation of an uncommon subcapsular variant of renal lymphangiomatosis, which failed percutaneous drainage.

Renal Lymphangiectasia Presenting with Polycythemia: Case Report

“…Yaş ve cinsiyet bakı-mından farklılık yoktur. 6,7 Bazı hastalarda ailesel geçiş bildirilmiştir. 8 Renal lenfanjiektazi asemptomatik kalabilmekte veya nonspesifik semptomlara neden olabilmektedir.…”

Renal lymphangiectasia presenting with hypertension and polycythemia

“…1 It is usually bilateral and asymptomatic, and unrelated to age or gender. 6,7 When symptomatic, it may be associated with abdominal/flank pain, hematuria, proteinuria, abdominal distension/mass, pleural effusion, weight loss, fatigue, renal failure, hypertension or polycythemia. 1 Familial occurrence has been described.…”

Percutaneous drainage and sclerotherapy as definitive treatment of

“…It is due to the failure of the perirenal lymphatic tissue to form normal communications with the remainder of the lymphatic system. 1 This leads to the dilation of lymphatic vessels and to the formation of unilocular or multilocular cystic masses in the perirenal area. Confusion exists in the literature.…”

“…2 Thirty-six cases are described in the English literature. 1, The differential diagnosis includes adult polycystic renal disease, von Hippel-Lindau disease, tuberose sclerosis, renal lymphoma with perirenal involvement and nephroblastomatosis. Computed tomography (CT) and magnetic resonance imaging (MRI) play a key role in the diagnosis, as the findings in RL are typical.…”