Reoperation After Supravalvular Aortic Stenosis Repair

Imamura, Michiaki; Prodhan, Parthak; Dossey, Amy M.; Jaquiss, Robert D.B.

doi:10.1016/j.athoracsur.2010.07.086

Cited by 27 publications

(26 citation statements)

References 14 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Ironically, assessment of the cardiovascular status of the patient often requires the use of sedation or anesthesia, thereby creating a clinical quandary, and numerous reports of cardiac arrest have occurred during these assessments. 25,26 Recommendations on the management of cardiovascular disease in WS have been published previously. 8 Table 1 outlines our recommended preprocedural management strategy.…”

Section: Recent Cardiologist Assessmentmentioning

confidence: 99%

Peri-procedural risk stratification and management of patients with Williams syndrome

Collins

Schmitz

et al. 2017

Congenital Heart Disease

View full text Add to dashboard Cite

Williams syndrome (WS) is a congenital, multisystem disorder affecting the cardiovascular, connective tissue, and central nervous systems in 1 in 10 000 live births. Cardiovascular involvement is the most common cause of morbidity and mortality in patients with WS, and noninvasive and invasive procedures are common. Sudden cardiovascular collapse in patients with WS is a well-known phenomenon, especially in the peri-procedural period. Detailed guidelines for peri-procedural management of patients with WS are limited. The goal of this review is to provide thoughtful, safe and effective management strategies for the peri-procedural care of patients with WS with careful consideration of hemodynamic impacts of anesthetic strategies. In addition, an expanded risk stratification system for anesthetic administration is provided.

show abstract

Section: Recent Cardiologist Assessmentmentioning

confidence: 99%

Peri-procedural risk stratification and management of patients with Williams syndrome

Collins

Schmitz

et al. 2017

Congenital Heart Disease

View full text Add to dashboard Cite

show abstract

“…Surgical outcome is heavily influenced by the presence of coronary tree anomalies (Eronem et al 2002 ; Imamura et al 2010 ; Hornik et al 2015 ). As a consequence, preoperative coronary tree evaluation is mandatory in all patients with WBS (Imamura et al 2010 ).…”

Section: Discussionmentioning

confidence: 99%

Multi-district coronary tree involvement in a 17-year-old girl with Williams–Beuren syndrome

et al. 2015

View full text Add to dashboard Cite

We describe a case of 17-year-old Chinese girl referred to our Pediatric Cardiology Unit for asthenia, reduced exercise tolerance, and dyspnea. Past medical history was relevant for multiple chest pain episodes in childhood and several syncopal episodes, for which the patient had been never evaluated. Clinical examination, electrocardiogram, and echocardiography were compatible with Williams–Beuren syndrome; such condition was later confirmed by genetic analysis. Cardiac magnetic resonance imaging showed transmural fibrosis of the apex with impaired left ventricular ejection fraction (29 %), severe stenosis of aortic sinotubular junction with left and right coronary ostia involvement; more importantly, the whole coronary artery tree beyond ostia was affected by multiple stenosis and aneurysmatic tracts. Ascending aorta proved hypoplastic, with post-stenotic dilation and multiple aneurysms. At the end of the diagnostic process, surgical risk was considered too high to proceed with the correction. The presented case is of educational value since it provides good iconographical illustration of diffuse, multiple-site coronary artery tree involvement, a rather rare co-morbidity in Williams–Beuren syndrome.Electronic supplementary materialThe online version of this article (doi:10.1186/s40064-015-1231-0) contains supplementary material, which is available to authorized users.

show abstract

“…Additionally, there was no pathology on the preoperative echocardiographic examination of the aortic valve. However, a study by Imamura et al [5] documented that the presence of aortic valve stenosis and a bicuspid aortic valve were risk factors for reoperation. Because of this, the pathology of the aortic leaflets may progress; therefore, echocardiographic follow-up is essential for monitoring this situation.…”

Section: Discussionmentioning

confidence: 99%

Repair of congenital supravalvular aortic stenosis in an adult patient

Sarıtaş¹

2013

Turk Gogus Kalp Dama

View full text Add to dashboard Cite

Supravalvüler aort stenozu (SVAS), aort kapağının üzerinde bulunan sol ventrikül çıkım yolu (SVÇY) obstrüktif lezyonlarının nadir görülen bir şeklidir. Nefes darlığı yakınması ile başvuran 45 yaşında bir erkek hastada önemli bir gradyana ve luminal daralmaya neden olan bir SVAS tespit edildi. Olgu iki sinüs rekonstrüksiyonu ve çıkan aort replasmanı ile başarılı bir şekilde tedavi edildi. Bu tür olgularda aort greft uygulamasının güvenli ve etkili bir işlem olabileceği kanısındayız.Anah tar söz cük ler: Çıkan aort; supravalvüler aort stenozu; cerrahi işlem.

show abstract

Reoperation After Supravalvular Aortic Stenosis Repair

Cited by 27 publications

References 14 publications

Peri-procedural risk stratification and management of patients with Williams syndrome

Peri-procedural risk stratification and management of patients with Williams syndrome

Multi-district coronary tree involvement in a 17-year-old girl with Williams–Beuren syndrome

Repair of congenital supravalvular aortic stenosis in an adult patient

Contact Info

Product

Resources

About