Report of a new‐born human presenting sympus dipus, anomalous umbilical vein, transposition of the viscera and other anomalies

Abstract

A survey of literature fails to reveal tlic i*eport of another ciise iii which synipus dipus, an anomalous umbilical w i n aid transposition of the viscei*a were associated. In reviewing the liteixturc thcse anonlalies will be coiisiclei*cd ilS sepiirate eiltities. REVIEW OFLlTERA'rCTRF: ~~J H~L S t1ipu.C. Various terms liave bccii i~yplied to the of iiiermaid rnonste1.s proposed in 1838 by Gcoffiq St.Hi1aii.c : 1. Symcle, iu wliicli tlic two lower extremities are almost perfectly nriited and terminate in R double foot, the sole of which is turriccl to\\.iird tlw front. 2. Uroiticle, in wliicli the two lower extremities arc very inconiplctcly united and termiiiitte in a single foot, usually vesy incomplete, the sole of which is turnecl toward the f roll t .3. Sirenorncle, in wliicli there is it rcry iiicomplcte union of botli lowcr extreiiiities which teriiiiiiatc iii il stump or in ti point without a distinct foot.Prosliek fui-tlier sttitecl tliut : Iii 1861, Foerstcr iiitroduced a dassifici~ tioii n4iich was very similar to tbilt of St. Hilaire. His termiiiology ~vas iiiore descriptive in character and is now more gciiewllp uscd in mermaid form of fetus. I'roshek ('25) citcd tlic classific~ <I t' 1011 34;

Persistent right umbilical vein: a prenatal condition worth mentioning?

“…Table S1 summarizes previous studies on PRUV published to date1–35. A total of 302 cases—including the present series—were reviewed.…”

Persistent right umbilical vein: incidence and significance

“…Among the different anomalies reported in association with PRUV are gastrointestinal malformations, various cardiac anomalies, skeletal malformations, urinary tract malformations and single umbilical artery 1,2,4,5,11 .…”

Prenatal diagnosis of a bifurcating umbilical vein with left iliac vein connection.

“…We are aware of 13 reported cases in which the ductus venosus was absent and the umbilical vein emptied directly into the systemic venous circulation. In these cases the umbilical vein joined the right atrium in five fetuses, 10,12,14,18,19 the inferior vena cava in four, 14,16,21,22 the left iliac vein in two, 15,17 and the right iliac vein in one fetus. 20 In the remaining case, the vein formed a caput medusa.…”

“…The ductus venosus (d) also is shown entering the right atrium. 13,17,21 Single umbilical artery 12,13,19 Hydranencephaly 15 Endocardial cushion defect 20 Situs inversus 10,14 Atrial septal defect 14 Total anomalous pulmonary venous return 16 Unilateral renal agenesis 16,19 Hydronephrosis 20 Unicornuate uterus 16 Hemivertebra 19 Sympus dipus 10 Phocomelia 16 Bifid thumb 19…”

“…In cases of absent ductus venosus, the umbilical venous circulation has been found to empty entirely into either the portal [5][6][7][8][9] or the systemic circulation. [10][11][12][13][14][15][16][17][18][19][20][21][22] We present a case diagnosed prenatally in which the umbilical vein bifurcated just outside the fetal abdominal wall, with one branch connecting to the left iliac vein and the other following a normal intrahepatic course connecting to the ductus venosus and left portal vein.…”