Retroperitoneal and Genital Lymphangioma: Therapeutic Challenges in a Developing Country

Abstract

Background: Lymphangiomas occur most commonly in the head and neck region, while other sites are rarely affected. A combination of retroperitoneal and genital lymphangioma is very rare indeed. Though congenital, it may persist into adulthood due to missed diagnosis and inadequate or total lack of treatment. Materials and methods: A report of a 22-year-old male student who presented with recurrent multiloculated genital, thigh, groin and retroperitneal lymphangioma. He underwent surgical excision and adjuvant sclerotherapy using ethylene-diamine tetra acetic acid. Results and Conclusions: There was an initial recurrence after surgery which responded satisfactorily to sclerotherapy. Complete surgical excision of lymphangioma may be precluded by vital structures but sclerotherapy produces satisfactory resolution. The difficulties in management with limited facilities for diagnosis and treatment are highlighted.

Giant retroperitoneal lymphangioma in a 70-year-old male: a case report

“…On small lymphangioma lesions, cryotherapy and electrocautery have been used. Carbon dioxide laser vaporization and the combination of laser light and radiofrequency energy are effective and relatively safe [ 13 - 15 ]. On histopathological examination, lymphangioma consists of cavities lined by an endothelium resting on fibrous tissue containing lymphocytic islets and sometimes smooth muscle fibers.…”

A rare case of thigh asymmetry in an infant

“…Moreover, the lesion described is confined only to the extremity, with no abdominal extension. Literature review reveals varied presentation of the entity such as juxta-articular lymphangioma of the extremity, 5 retroperitoneal and genital lymphangioma, 6 and even acquired cases of progressive lymphangioma. 7 Previously published case reports documented abdominal lymphatic malformations extending to the extremities, mostly in autopsy specimens of preterm infants after termination of pregnancy.…”