Right pulmonary venous atresia: a case report and review of literature

Abstract

ÖZET Sağ pulmoner ven atrezisi: Olgu sunumu ve literatürün gözden geçirilmesi

Isolated unilateral pulmonary vein atresia with hemoptysis in a child

“…The other considerable option is pneumonectomy suitable for patients with severe symptoms and signs to obviate the life-threatening complications such as recurrent severe respiratory tract infections, pulmonary hypertension and/or recurrent hemoptysis. [ 12 , 15 ] Available evidence indicates that the outcome of pulmonary resection is satisfactory. Nevertheless, pneumonectomy is burdened with increased morbidity in small growing children, like scoliosis, kyphosis, or unilateral hypoplastic chest wall, all being more pronounced when the child is younger.…”

Isolated agenesis of the right pulmonary veins with pulmonary sequestration

“…Atresia of unilateral PVs is a rare anomaly and nearly 50 cases were reported in the literature. [6] About 30%–50% are associated with other abnormalities, namely septal defects and complex anomalies such as single ventricle, veno-occlusive disease, and Scimitar syndrome. [789]…”

Unilateral Pulmonary Vein Atresia with Contralateral Upper Pulmonary Vein Atresia in an Adult Patient

“…Since our patient was still alive and did not undergo surgery, pathological correlation was not available, which is a limitation of this report. Follow-up of patients with few or no symptoms [8,16] and selective embolization of systemic collaterals in cases of hemoptysis [4] are therapeutic options. Pneumonectomy guided by ventilation perfusion scintigraphy [13] may be suggested to inpatients with dyspnea, recurrent infections and to prevent pulmonary hypertension without significant left to right shunt [7,8].…”