Right ventricular myxoma obstructing the pulmonary artery during early childhood

Abstract

Primary cardiac tumors are uncommon during infancy and childhood. Myxomas originating in the right ventricle are even less common in pediatric patients. A 2-year-old girl was referred to our hospital under a diagnosis of right ventricular tumor. The aim of the operation was extirpation of the tumor. Perioperative cardiac arrest occurred when the tumor obstructed the pulmonary artery. After promptly establishing cardiopulmonary bypass, the tumor was removed from the right ventricular outflow tract. The patient was discharged on the 13th postoperative day without complications.

Pulmonary artery obstruction due to a metastatic malignant phyllodes tumor of the breast

“…Moreover, if total main pulmonary artery occlusion occurred, the patient's heart would stop suddenly. 3 We therefore thought that releasing the severe stenosis of the main pulmonary artery might offer her longer survival. 4 As a result, we scheduled palliative surgery for the next day.…”

Multimodality imaging of a subtotally obstructive right ventricular myxoma in an asymptomatic 10-year-old girl

“…[23] Myxomas that arise in the right ventricle and obstruct the right ventricular outflow tract are extremely rare in children, and there are only isolated reports of such cases. [456]…”

Myxoma of right ventricular outflow tract with pulmonary artery obstruction

“…Around 80% of the myxomas are localized to the left atrium. Reports of myxomas arising from the right ventricular outflow tract are extremely rare and up to now only few cases have been reported in the literature [1][2][3][4][5] and in some cases the tumors were multiple or biventricular 1,2 . In majority of cases the presentation was acute, either in form of acute right ventricular failure 1 or multiple syncopal attacks or cardiac arrest 3 .…”

“…They are rarely found in the ventricles. Myxomas in the Right Ventricular Outflow Tract (RVOT) are very rarely reported [1][2][3][4][5] . We present one such case where the myxoma was arising from the right ventricular outflow tract, partially involving the pulmonary valve and causing obstruction of the right ventricular outflow tract.…”