Robotic mitral valve repair in a type B hemophiliac

Abstract

Hemophilia B is a rare X-linked recessive disorder that places surgical patients at an increased risk of bleeding. Patients with hemophilia are now achieving near-normal life expectancies and therefore the number of these patients requiring cardiac surgery due to the development of age-related cardiovascular disease may increase.We present the case of a young male with hemophilia B who was diagnosed with severe symptomatic mitral regurgitation and underwent successful robotic mitral valve repair. To our knowledge, this is the first report of a patient with hemophilia B who underwent robotic mitral valve repair. K E Y W O R D S replacement, valve repair

Minimally invasive mitral valve repair and ablation of concomitant atrial fibrillation in a patient with severe hemophilia A

“…The literature presents a few cases of mitral valve reconstruction in hemophilia A patients. 4 , 5 , 6 , 7 Only one describes a minimally invasive mitral valve repair with concomitant atrium ablation. 8 Minimally invasive approach for mitral valve surgery has advantages over standard sternotomy, which may be especially important in patients with bleeding disorders.…”

“…In the case of mitral insufficiency in young patients, valve repair is preferable to valve replacement as it potentially avoids the need for short‐term anticoagulation treatment. The literature presents a few cases of mitral valve reconstruction in hemophilia A patients 4‐7 . Only one describes a minimally invasive mitral valve repair with concomitant atrium ablation 8 .…”

Modern Treatment of Valvulopathies in Patients with Congenital Hemophilia

“…One of them had MV prolapse and moderate-to-severe MR due to rupture of a tendinae [ 5 ]. In two patients, MV flail was identified [ 16 , 17 ]. Aortic valve replacement (AVR) for stenosis was performed in four patients [ 18 , 19 , 20 , 21 ], one of them with a bicuspid valve.…”

“…In two cases, MV repair was performed concurrently with CABG [ 5 , 29 ], and in one case, with the resection of a left ventricular aneurysm [ 30 ]. Artificial chordae were necessary for three patients [ 5 , 16 , 17 ]. Insertion of an annuloplasty system—ring or band—was performed in five patients [ 5 , 15 , 16 , 17 , 29 ].…”

“…Artificial chordae were necessary for three patients [ 5 , 16 , 17 ]. Insertion of an annuloplasty system—ring or band—was performed in five patients [ 5 , 15 , 16 , 17 , 29 ]. In general, recovery after MV repair interventions was uneventful.…”