Ruptured sinus of Valsalva aneurysm with tetralogy of Fallot in an adult

Abstract

A combination of ruptured sinus of Valsalva (RSOV) aneurysm with tetralogy of Fallot (TOF) is a very rare condition. We report a 32-year-old male who underwent repair of a RSOV aneurysm with TOF.

Ruptured sinus of valsalva presenting late following repair of tetralogy of fallot

“…5 RSOV can also present with symptoms of congestive cardiac failure and remains a rare but important entity in these patients following TOF repair. [3][4][5] Infective endocarditis is a major acquired cause of RSOV 1 and is indicated in this patient by prolonged high grade fever 1 month after surgery. Treatment of RSOV includes surgical closure or closure with an occluder device.…”

“…Only six cases of TOF with RSOV have been reported. 3,4 Three of these had repair of TOF before appearance of RSOV. 3,4 RSOV was diagnosed in two patients at 3 and 10 years, respectively after repair of TOF.…”

“…Important causes of pleural effusion following repair of TOF are residual ventricular septal defect, severe tricuspid regurgitation, major aortopulmonary collaterals, residual RVOT obstruction, and aortic regurgitation 5 . RSOV can also present with symptoms of congestive cardiac failure and remains a rare but important entity in these patients following TOF repair 3‐5 …”

“…Besides being a developmental anomaly, acquired causes are endocarditis, atherosclerosis and cystic medial necrosis 1 . RSOV is rarely associated with tetralogy of fallot (TOF) 3,4 . We report a 16‐year‐old boy who developed RSOV 4 months after uneventful repair of TOF.…”

“…1 RSOV is rarely associated with tetralogy of fallot (TOF). 3,4 We report a 16-year-old boy who developed RSOV 4 months after uneventful repair of TOF.…”