S-shaped Kidney: A Rare Occurrence of Supernumerary Kidney with Fusion-malrotation

Bilaterally Fused Supernumerary Kidneys: A Very Rare Case Report and Review of Literature

“…12 One might encounter a diagnostic confusion between SNK and a duplex kidney, the later one being more common and characterized by renal unit contained within a single capsule with the same (single) vascular supply as the contralateral kidney. 3,13 The total number of calices in a SNK and the ipsilateral kidney is higher than that of the contralateral kidney. 14,15 Joseph F. Geisinger (1937) wrote a comprehensive review of literature regarding 40 patients with this anomaly and characterized SNK as; "a rare scenario that resulted from a lawless embryological sequence", to describe the lack of consistency in its anatomic appearance and physiologic function.…”

“…When SNK is located caudally, a bifid ureter is seen often and the common site of fusion is usually near the bladder. [4][5][6][7][8][9][10][11][12][13][14][15][16][17] The Weigert-Meyer rule may be followed in SNKs with ectopically located ureteric orifices during entry into the bladder but rare reports of opening near the vagina, cervix, prostatic urethra and vulva also exist. 18 The embryological development of SNK has been debated in the literature.…”

“…2,9,17,19 Our patient had an additional rotational anomaly of both SNKs likely due to an abnormally late ureteric bud insertion. 13 No associated anomaly is diagnosed in other organ systems of the patient, but there are reports of concomitant urologic and non-urologic anomalies in patients with SNK. These include: vaginal atresia, urethral duplication, penile duplication, horseshoe kidney, ventricular septal defects, coarctation of aorta, megaureter, imperforate anus, and meningomyelocele.…”

Fused Right Supernumerary Kidney: A Case Report

“…Supernumerary kidney however has a separate arterial supply, venous drainage, collecting system and is either totally separate from the normal kidney or connected to it by loose areolar tissue. 4 - 7 …”

“…Supernumerary kidney however has a separate arterial supply, venous drainage, collecting system and is either totally separate from the normal kidney or connected to it by loose areolar tissue. [4][5][6][7] Pathologies of the urinary tract have been reported in patients with supernumerary kidneys with nephrolithiasis and hydronephrosis being common. 3 In our case as well, large calculi were noted in the fused right supernumerary kidney.…”