Sarcoma indiferenciado (embrionario) de hígado del adulto: informe de un caso y revisión de la literatura médica

Fuertes, Montiel Jiménez; Andújar, Rafael López; Burgueño, Manuel de Juan; Herráiz, Ángel Moya; Rodriguez, Fernando S. Reina; Orón, Eva Montalvá; Ibars, Eugenia Pareja; Pallardó, José Mir

doi:10.1157/13114564

Cited by 7 publications

(2 citation statements)

References 28 publications

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“…They represent a heterogeneous group of neoplasms including undifferentiated embryonal sarcoma (UESL), which was first described by Stocker and Ishak2 in 1978 as a mesenchymal tumor without any specific differentiation. Until now, few adult patients with UESL have been reported in the literature, with a slight preference for females and a mean age at diagnosis of 51 3. Although UESL is associated with prognosis with a reported survival time of less than one year, early diagnosis is essential to increase the overall survival 4…”

Section: Introductionmentioning

confidence: 99%

Undifferentiated embryonal sarcoma of the liver in adult patient: A report of two cases

Sánchez-Morales

Emilio

Alvarez-Bautista

et al. 2018

Ann Hepatobiliary Pancreat Surg

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Primary sarcomas of the liver are unusual neoplasms developing in adults. They constitute a heterogeneous group of neoplasms including undifferentiated embryonal sarcoma. Patients usually present with an abdominal mass and abdominal pain. Case 1: A 53-year-old woman presented with abdominal pain. Computed tomography showed an occupying mass in the right lobule and an intra-auricular multi-lobulated mass suggestive of a secondary deposit. Biopsy of the hepatic lesion revealed undifferentiated embryonal sarcoma. Despite radiotherapy and supportive measures, her overall status progressively worsened until cardiac arrest. Case 2: A 41-year-old woman presented with hepatomegaly. Abdominal imaging showed cystic lesions in the right hepatic lobule with multiple septae. The patient underwent extended right hepatectomy and a histopathological study reported high-grade undifferentiated embryonal sarcoma. Two years after surgery, a new cystic lesion in the surgical site was recorded and chemotherapy was scheduled. The lesion remained stable for three years when disease progression was observed and second-line chemotherapy was initiated. Although undifferentiated embryonal sarcoma of the liver has poor prognosis, early diagnosis is essential to increase the chances of survival. Currently, surgical resection and chemotherapy are the primary treatment modalities.

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Section: Introductionmentioning

confidence: 99%

Undifferentiated embryonal sarcoma of the liver in adult patient: A report of two cases

Sánchez-Morales

Emilio

Alvarez-Bautista

et al. 2018

Ann Hepatobiliary Pancreat Surg

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“…A recent review of the literature showed only 70 cases of UES in adults reported worldwide in 2008 2. This rare presentation is especially true for adults aged >60 years with only 14 cases of UES reported in this population until now 3,4,5,6,7.…”

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confidence: 99%

Undifferentiated Embryonal Sarcoma in Adult Liver

Hong

Kang

2014

Korean J Pathol

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Undifferentiated Embryonal Sarcoma of the Liver: First Case Reported in Central America

García,

Fonseca,

del Rosario Romero Alvarez

2024

Cancer Reports

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BackgroundUndifferentiated embryonal sarcoma of the liver (UESL) is a rare and aggressive mesenchymal tumor, typically occurring in children. It poses significant diagnostic challenges due to its atypical presentation and rarity in clinical practice.CaseWe report the first case in Central America of a 19‐year‐old female presenting with chronic abdominal pain and a liver mass. Imaging revealed a solid and cystic lesion in the liver, and a subsequent complete surgical resection confirmed the diagnosis of UESL. The patient received adjuvant chemotherapy and has been disease‐free for 34 months.ConclusionThis case highlights the importance of complete surgical resection combined with chemotherapy to improve prognosis in UESL. Our findings emphasize the need to consider UESL in differential diagnoses of liver lesions, especially in regions where it has not been previously reported.

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Sarcoma indiferenciado (embrionario) de hígado del adulto: informe de un caso y revisión de la literatura médica

Cited by 7 publications

References 28 publications

Undifferentiated embryonal sarcoma of the liver in adult patient: A report of two cases

Undifferentiated embryonal sarcoma of the liver in adult patient: A report of two cases

Undifferentiated Embryonal Sarcoma in Adult Liver

Undifferentiated Embryonal Sarcoma of the Liver: First Case Reported in Central America

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