Scleredema adultorum of Buschke presenting as periorbital edema: A diagnostic challenge

Angiœdème : diagnostics différentiels

“…Dans sa forme diffuse, elle ne pose pas de problème de diagnostic différentiel avec un angioedème. En revanche, des formes plus localisées, par exemple aux paupières [18], peuvent initialement mimer un angioedème mais le caractère permanent permet de redresser le diagnostic. Dermatomyosite et lupus La dermatomyosite peut s'accompagner d'oedème des paupiè-res, parfois intermittent.…”

Scleredema adultorum of Buschke over an unusual site associated with pregnancy

“…Involvement of unusual sites like periorbital area and thighs has been reported in the literature. [67] Here, we report a rare case of scleredema over the lower abdomen and thighs in a pregnant woman, associated with streptococcal upper respiratory tract infection.…”

Periorbital edema

“…There are a number of other even rarer inflammatory disorders, such as cold urticaria [49], relapsing polychondritis [50], lymphedematous rosacea [51,52], allergic eosinophilic gastroenterocolitis [53], Melkerson-Rosenthal syndrome [54,55], polyarteritis nodosa [56], cutis laxa [57], scleredema adultorum of Buschke [58], dermatographism [59], and tumor necrosis factor receptor-associated periodic syndrome [60]. These entities should be considered when the more common causes of periorbital edema are ruled out.…”