Segmental Dilatation of the Ileum Covered Almost Entirely by Gastric Mucosa: Report of a Case

Kobayashi, Tsutomu; Uchida, Nobuyuki; Shiojima, Masayuki; Sasamoto, Hajime; Shimura, Tatsuo; Takahasi, Atsusi; Kuwano, Hiroyuki

doi:10.1007/s00595-007-3526-4

Cited by 12 publications

(9 citation statements)

References 9 publications

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“…Other than hypertrophic or very thin muscle layers in the involved segment, ectopic tissue, such as the gastric or pancreatic tissue, was demonstrated. 8 27 50 Gastric adenomyoma of the pyloric region should be considered a differential diagnosis of hypertrophic pyloric stenosis and gastric duplication in newborns and children. 51 52…”

Section: Discussionmentioning

confidence: 99%

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Congenital Segmental Intestinal Dilatation: A 25-Year Review with Long-Term Follow-up at the Medical University of Innsbruck, Austria

Sergi

Hager

2019

AJP Rep

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Background and Aim Congenital segmental intestinal dilatation (CSID) is a neonatal condition with unclear etiology and pathogenesis. Typically, the newborn with CSID presents with a limited (circumscribed) bowel dilatation, an abrupt transition between normal and dilated segments, neither intrinsic nor extrinsic perilesional obstruction, and no aganglionosis or neuronal intestinal dysplasia. We aimed to review this disease and the long-term follow-up at the Children's Hospital of the Medical University of Innsbruck, Tyrol, Austria. Study Design Retrospective 25-year review of medical charts, electronic files, and histopathology of neonates with CSID. Results We identified four infants (three girls and one boy) with CSID. The affected areas included duodenum, ileum, ascending colon, and sigmoid colon. Noteworthy, all patients presented with a cardiovascular defect, of which two required multiple cardiac surgical interventions. Three out of the four patients recovered completely. To date, the three infants are alive. Conclusion This is the first report of patients with CSID and cardiovascular defects. The clinical and surgical intervention for CSID also requires a thorough cardiologic evaluation in these patients. CSID remains an enigmatic entity pointing to the need for joint forces in identifying common loci for genetic investigations.

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Section: Discussionmentioning

confidence: 99%

“…This entity remains enigmatic and challenging because of the ambiguous clinical findings, nonspecific radiological examinations, and mimickers of the urinary tract. 50 70…”

Section: Discussionmentioning

confidence: 99%

Congenital Segmental Intestinal Dilatation: A 25-Year Review with Long-Term Follow-up at the Medical University of Innsbruck, Austria

Sergi

Hager

2019

AJP Rep

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“…Several theories were proposed to explain this malformation; however, most authors are rather inclined to an embryological theory incriminating an extrinsic intrauterine intestinal compression. [678910] In our case we found a band connecting posterior aspect of umbilicus to the dilated part of the small bowel but not found causing compression of gut. Pathological examination shows a bowel wall with all layers as well as a normal ganglion cells.…”

Section: Discussionmentioning

confidence: 50%

Congenital segmental dilatation of jejunoileal region in a newborn: Unusual clinical and radiologic presentation

Harjai

Katiyar

Negi

et al. 2010

J Indian Assoc Pediatr Surg

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Segmental dilatation of the ileum is one of the uncommon causes of intestinal obstruction in neonates. We present a case of slow transit of bowel contents leading to suspicion of functional bowel obstruction in a new born, which on exploration turned out to be a case of segmental dilatation of the jejuno-ileal region. The clinical and radiological evaluation was suggestive of hypomotility disorder of gut, resulting in diagnostic dilemma and delayed surgical intervention.

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“…Heterotopic esophageal or gastric mucosa or cartilaginous foci are also reported in dilated intestinal segment [ 3 ]. Kobayashi et al suggested that ectopic gastric mucosa causes interruption in the neural and muscular network in the dilated intestine [ 14 ]. However, all resected segments show normal presence of ganglion cells in myenteric and submucosal plexuses [ 6 ].…”

Section: Discussionmentioning

confidence: 99%

Segmental ileal dilatation with supernumerary intestinal muscle coat in a neonate

2015

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Segmental intestinal dilatation (SID) is a rare developmental anomaly of the midgut, characterized by sharply demarcated dilatation of a gastrointestinal segment with clinical findings of intestinal obstruction. Although morphologic criteria for SID are clearly delineated, etiological origin of dilated intestine is unknown. Histology of the resected segment is usually reported to have normal presence of ganglion cells in the myenteric and submucosal plexuses. Intestinal muscle is hypertrophied, and heterotopic gastric mucosa may also be encountered. A 3-day-old male infant presenting with clinical findings of intestinal obstruction was diagnosed to have SID and had supernumerary intestinal muscle coat (SIMC) in the dilated segment, without any evidence of neurological abnormality. Histopathological findings of the resected ileal segment are reported to discuss the role of architectural malformation of muscularis propria as a cause of SID.

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Segmental Dilatation of the Ileum Covered Almost Entirely by Gastric Mucosa: Report of a Case

Cited by 12 publications

References 9 publications

Congenital Segmental Intestinal Dilatation: A 25-Year Review with Long-Term Follow-up at the Medical University of Innsbruck, Austria

Congenital Segmental Intestinal Dilatation: A 25-Year Review with Long-Term Follow-up at the Medical University of Innsbruck, Austria

Congenital segmental dilatation of jejunoileal region in a newborn: Unusual clinical and radiologic presentation

Segmental ileal dilatation with supernumerary intestinal muscle coat in a neonate

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