Síndrome de Susac. Caso clínico y revisión

Y, Phoebe Ramos; H, Leandro Rodríguez; C, Carolina Peralta; S, Francisca Montoya

doi:10.4067/s0717-75262018000200167

Cited by 1 publication

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“…Se estima que se trata de una enfermedad con etiología microangiopática autoinmunitaria de los endotelios vasculares que provoca la oclusión de ramas arteriales. (1,2,3) Debido a que representa un reto diagnóstico esta enfermedad no puede ser detectada en etapas iniciales por lo que se utilizan diversos métodos diagnósticos en función de las manifestaciones clínicas, datos de laboratorio, estudios de imagen y audiometría. Por lo tanto, es esencial realizar un diagnóstico diferencial robusto para diferenciarlo de otro tipo de patologías.…”

Section: Introductionunclassified

Management of Susac Syndrome

Chamba

Garzón

Jiménez

et al. 2022

Salud, Ciencia y Tecnología

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Introduction: Susac syndrome is a disease with autoimmune microangiopathic etiology of vascular endothelia that causes occlusion of arterial branches. Due to its high diagnostic complexity, it cannot be detected at the onset of the syndrome because most patients do not present the characteristic triad at a certain time, they start their picture with neurological manifestations which implies several differential diagnoses. Aim: To describe the correct management of Susac Syndrome based on the main diagnostic criteria and the efficacy of pharmacological treatment. Methods: A literature review study of articles from 2017 to 2022 on Susac syndrome was conducted in the following databases: Scopus, SciELO, Pubmed, Cochrane and Lilacs. Results: This disease is characterized by the presence of a pathognomonic triad of encephalopathy, sensorineural hearing loss and retinal arterial occlusion. Consequently, it is vital to use different diagnostic methods: laboratory data, imaging studies and audiometry. Treatment regimens have been proposed, establishing corticosteroids and immunomodulators as the first line of treatment. When considering pharmacological treatments, not only the severity of SS must be contemplate but also the presence of comorbidities and characteristics according to each patient in order to define the appropriate pharmacological scheme for each patient. Conclusions: Audiometric examinations are considered fundamental for the diagnosis since sensorineural hearing loss can be evidenced in low and medium frequencies, it is important to perform surgical interventions with the purpose of avoiding the progression of the syndrome.

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Section: Introductionunclassified