Staged Corrective Surgery for a Patient With Sagittal Malalignment Related to Noonan Syndrome

Abstract

Case:A 20-year-old man with Noonan syndrome had rigid cervical kyphosis caused by cervical myelopathy and thoracic lordosis caused by pulmonary disfunction. Two-staged corrective surgery, which involved initial posterior spinal fusion (PSF) in T2-L2 followed by PSF in C3-T2, had been performed without any complications. The radiographs before surgery and 2 years after surgery showed that cervical lordosis (C2-7) changed form −56° to −29°, and thoracic kyphosis (T5-12) improved from −49° to 10°.Conclusion:Initial realignment surgery in the caudal lesion should be better for improving global spinal alignment in patients with rigid spinal deformities at different locations.