Steatocystoma multiplex: appearance at mammography.

Abstract

The authors present mammographic findings in a patient with steatocystoma multiplex. Numerous oil cysts were seen in both breasts at mammography. The mammographic appearance is characteristic of, if not pathognomonic for, steatocystoma multiplex.

Steatocystoma Multiplex: Mammographic and Sonographic Manifestations

“…In our study, the lesions varied in color from fleshy to yellow [1,[6][7][8][9]. The more superficial lesions were yellow and prominent; deeper lesions were not visible and were skin-colored [8].…”

“…Steatocystoma multiplex is a rare familial hamartomatous malformation of the piloseba- ceous duct junction that is characterized by the presence of multiple intradermal cysts that usually appear during adolescence and then progress [1,[5][6][7][8][9]. Although both sexes are equally affected, some authors have reported a greater prevalence in males [5].…”

“…Only a few case reports have been published that detail the radiologic features of pathologically proven steatocystoma multiplex [7][8][9]. Hence, we present its typical clinical manifestations and imaging features as a diagnostic aid.…”

“…Pathologically, the nodules are composed of small keratin-filled cysts located in the mid dermis that contain numerous transversely or obliquely cut vellus hair shafts [2]. The condition, which is often inherited as an autosomal dominant trait [3][4][5][6][7][8], affects both sexes [1,7].The diagnosis is usually established clinically, although biopsy may be required. Only a few case reports have been published that detail the radiologic features of pathologically proven steatocystoma multiplex [7][8][9].…”

“…Pathologically, the nodules are composed of small keratin-filled cysts located in the mid dermis that contain numerous transversely or obliquely cut vellus hair shafts [2]. The condition, which is often inherited as an autosomal dominant trait [3][4][5][6][7][8], affects both sexes [1,7].…”