Subjective Oral Health-Related Quality of Life and Objective Oral Health in People with Ectodermal Dysplasia

Abstract

Ectodermal dysplasia (ED) refers to a heterogeneous group of genetic diseases of the skin, skin appendages, and teeth. People with ED experience a poorer oral health-related quality of life (OHRQoL) compared to the general population. The aim of this study was to examine the OHRQoL of people with ED and to measure their objective physical oral health to confirm or disprove evidence of poorer oral health in this population. To determine OHRQoL, the German version of the 14-item Oral Health Impact Profile (OHIP-14G) was used. All the participants in the study were clinically examined, and the measured parameters were recorded using the Physical Oral Health Index (PhOX). In total, 10 male and 11 female participants, with an average age of 22.0 ± 9.0 years, were included in this study. The OHIP-14G summary score was 23.9 (±15.2) points (range: 0–56 points). The PhOX summary score was 61.2 (±5.1) points (range: 22–80 points). The findings indicated that both the OHRQoL and physical oral health of the participants were highly impaired and that their objective and subjective oral health were worse than those of the general population in Germany.

Digital Implant Planning in Patients with Ectodermal Dysplasia: Clinical Report

“…Our research group previously showed that people diagnosed with oral abnormalities as manifestations of rare diseases are less satisfied with their oral situation than the general population [14,15]. In this regard, the oral rehabilitation with fixed implant-supported prosthodontics seems to improve the perception about their oral-health quality of life [16].…”

“…Radiological examinations showed a reduced bone height at the edentulous site. In consideration of a bone atrophy in the upper and lower jaws, a two-stage surgical procedure was planned, which included bilateral sinus lift, nerve lateralization and placement of dental implants at the sites 16,15,12,22,35,36,32,42, and 45 (Figure 2). aesthetic and functional complaint.…”

“…Radiological examinations showed a reduced bone height a edentulous site. In consideration of a bone atrophy in the upper and lower jaws, a stage surgical procedure was planned, which included bilateral sinus lift, n lateralization and placement of dental implants at the sites 16,15,12,22,35,36,32, 42 45 (Figure 2). The first surgical procedure included nerve lateralization at the left lower jaw, sinus lift, and placement of dental implants in edentulous sites with adequate bone volume.…”

Parental perception on oral health-related quality of life and dental features of ectodermal dysplasia and isolated hypodontia in children

“…The current literature reports a substantial negative impact for severe hypodontia, both syndromic and isolated, regardless of the instrument used to assess OHRQoL [ 5 , 6 , 22 – 25 ]. The findings from our study are in agreement with the literature, parents from both the ED and IH groups reported a high impact on QoL.…”

Versorgungsforschung in der Zahnmedizin in Deutschland

“…Die Polikliniken für Zahnerhaltung an den Universitätskliniken Freiburg, Göttingen (gemeinsam mit der Zahnersatzkunde) und Leipzig haben praxisbasierte Forschungsnetzwerke geschaffen [ 8 ]; letzterer Verbund widmet sich schwerpunktmäßig den Zusammenhängen von Zahnmedizin und chronischen Allgemeinerkrankungen [ 16 , 17 ]. Weiter finden sich Aktivitäten an der Universität Münster – etwa zum Register Oraler Manifestationen Seltener Erkrankungen [ 18 ] – und der Universitätszahnklinik Witten/Herdecke, u. a. zu den Themen „Zuckerkonsum“ und „Menschen mit Behinderung“ [ 19 ].…”