Successful chemotherapy for melanotic neuroectodermal tumor of infancy in a baby

Abstract

Fig. 2. Coronal CT scan of the face at the age of 24 months.

Melanotic neuroectodermal tumour of infancy (progonoma) treated by radical maxillary surgery

“…8 No adjuvant chemotherapy is currently recommended 1 although chemotherapy has been tried in some cases that were not surgically resectable with varying response. 9,10,11 . Two cases of MNTI managed successfully with surgical excision alone are presented here.…”

Melanotic neuroectodermal tumor in a newborn

“…So early diagnosis, early management and frequent follow-up are very important in MNTI. Radiotherapy and chemotherapy have been suggested in those cases where total resection could not be achieved and recurrence or metastatic disease was encountered [11].…”

Melanotic Neuroectodermal Tumor of Infancy

“…In instances of inoperable recurrence or where clear margins are impossible to obtain, radiation therapy and/or chemotherapy have been used, but too few examples exist for preferences to be established. 6 Permanent reconstruction of the maxillary alveolus and missing dentition may have to be delayed until after growth is completed, often in the teenage years. In the interim, transitional removable partial dentures may be necessary.…”