2005
DOI: 10.1097/01.pas.0000146014.22624.8e
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Superficial Low-grade Fibromyxoid Sarcoma (Evans Tumor)

Abstract: Low-grade fibromyxoid sarcoma (LGFMS), usually a deeply situated mass in adults, is uncommon in superficial soft tissue and in children. Nineteen superficial LGFMS from our files were studied for clinicopathologic features, the latter including tumor size, growth pattern, cellularity, collagen rosettes, vascularity, nuclear atypia, mitotic rate, necrosis, and immunophenotype. The patients included 12 males and 7 females who ranged in age from 2 to 70 years (mean, 29 years). There were 7 children. Tumor locatio… Show more

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Cited by 173 publications
(63 citation statements)
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“…LGFMS tends to be located superficially in young patients, whereas deep LGFMS accounts for the majority of adult cases [1,7]. Superficial LGFMS was reported to account for no more than 10% of LGFMS cases in all ages [4]; however, it was found in 73% of the patients 15 years and younger in our literature review, in line with the previous finding [22]. Particularly, in patients 5 years of age or younger in which information for the depth of the tumor was available, all cases were located superficially, and our case was the only one that was deeply located.…”
Section: Discussionsupporting
confidence: 89%
“…LGFMS tends to be located superficially in young patients, whereas deep LGFMS accounts for the majority of adult cases [1,7]. Superficial LGFMS was reported to account for no more than 10% of LGFMS cases in all ages [4]; however, it was found in 73% of the patients 15 years and younger in our literature review, in line with the previous finding [22]. Particularly, in patients 5 years of age or younger in which information for the depth of the tumor was available, all cases were located superficially, and our case was the only one that was deeply located.…”
Section: Discussionsupporting
confidence: 89%
“…Low grade fibromyxoid sarcoma (LGFMS) is a rare soft tissue sarcoma characterized by relatively benign histology with fibrous paucicellular and myxoid hypervascular zones (1). In the short term (< 5 years), LGFMS has an indolent clinical behavior but also a tendency for late local recurrence and metastasis (2).…”
Section: Introductionmentioning
confidence: 99%
“…The latter location is more commonly seen in children relative to adults. On cytogenetic studies, these tumors have a t(7;16)(q34;p11) translocation (1). Cross-sectional imagaing, such as computed tomography (CT) and magnetic resonance imaging (MRI), has played a crucial role in the detection, evaluation of local extent, and staging of soft tissue tumors.…”
Section: Introductionmentioning
confidence: 99%
“…The category of fibrosarcoma has been expanded to include a number of distinct subtypes 12. Evans in 1987 described a distinctive form of fibrosarcoma that he called ‘low-grade fibromyxoid sarcoma’ (LGFMS) 34. A decade after these seminal studies, Lane et al described the entity called ‘hyalinizing spindle cell tumor with giant rosettes’ (HSCTGR) 2.…”
Section: Discussionmentioning
confidence: 99%
“…These are rare sarcomas which are commonly seen in young to middle-aged adults and typically occur in a subfascial location in the proximal extremities or trunk as painless, deep-seated, slowly-enlarging soft tissue masses 145. Grossly, the tumor is an oval multilobulated mass, ranging in size from 2 to 20 cm in diameter.…”
Section: Discussionmentioning
confidence: 99%